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INTERNATIONAL CLASSIFICATION OF DISEASES

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vertical line Table of Contents Alphabetical Index of Diseases and Injuries Explanation of Disease Classification

6. Diseases of the Nervous System and Sense Organs (320-389)




INFLAMMATORY DISEASES OF THE CENTRAL NERVOUS SYSTEM (320-326)

320	Bacterial meningitis
Includes:	arachnoiditis bacterial
leptomeningitis bacterial
meningitis bacterial
meningoencephalitis bacterial
meningomyelitis bacterial
pachymeningitis bacterial
320.0	Hemophilus meningitis
Meningitis due to Hemophilus influenzae [H. influenzae]
320.1	Pneumococcal meningitis
320.2	Streptococcal meningitis
320.3	Staphylococcal meningitis
320.7	Meningitis in other bacterial diseases classified elsewhere
Code first underlying disease as:
actinomycosis (039.8)
listeriosis (027.0)
typhoid fever (002.0)
whooping cough (033.0-033.9)
Excludes:	meningitis (in):
epidemic (036.0)
gonococcal (098.82)
meningococcal (036.0)
salmonellosis (003.21)
syphilis:
NOS (094.2)
congenital (090.42)
meningovascular (094.2)
secondary (091.81)
tuberculosis (013.0)
320.8	Meningitis due to other specified bacteria
320.81	Anaerobic meningitis
Gram-negative anaerobes
Bacteroides (fragilis)
320.82	Meningitis due to gram-negative bacteria, not elsewhere classified
Aerobacter aerogenes
Escherichia coli [E. coli]
Friedlander bacillus
Klebsiella pneumoniae
Proteus morganii
Pseudomonas
Excludes:	gram-negative anaerobes (320.81)
320.89	Meningitis due to other specified bacteria
Bacillus pyocyaneus
320.9	Meningitis due to unspecified bacterium
Meningitis:
bacterial NOS
purulent NOS
pyogenic NOS
suppurative NOS
321	Meningitis due to other organisms
Includes:	arachnoiditis due to organisms other than bacteria
leptomeningitis due to organisms other than bacteria
meningitis due to organisms other than bacteria
pachymeningitis due to organisms other than bacteria
321.0	Cryptococcal meningitis
Code first underlying disease (117.5)
321.1	Meningitis in other fungal diseases
Code first underlying disease (110.0-118)
Excludes:	meningitis in:
candidiasis (112.83)
coccidioidomycosis (114.2)
histoplasmosis (115.01, 115.11, 115.91)
321.2	Meningitis due to viruses not elsewhere classified
Code first underlying disease, as:
meningitis due to arbovirus (060.0-066.9)
Excludes:	meningitis (due to):
abacterial (047.0-047.9)
adenovirus (049.1)
aseptic NOS (047.9)
Coxsackie (virus) (047.0)
ECHO virus (047.1)
enterovirus (047.0-047.9)
herpes simplex virus (054.72)
herpes zoster virus (053.0)
lymphocytic choriomeningitis virus (049.0)
mumps (072.1)
viral NOS (047.9)
meningo-eruptive syndrome (047.1)
321.3	Meningitis due to trypanosomiasis
Code first underlying disease (086.0-086.9)
321.4	Meningitis in sarcoidosis
Code first underlying disease (135)
321.8	Meningitis due to other nonbacterial organisms classified elsewhere
Code first underlying disease
Excludes:	leptospiral meningitis (100.81)
322	Meningitis of unspecified cause
Includes:	arachnoiditis with no organism specified as cause
leptomeningitis with no organism specified as cause
meningitis with no organism specified as cause
pachymeningitis with no organism specified as cause
322.0	Nonpyogenic meningitis
Meningitis with clear cerebrospinal fluid
322.1	Eosinophilic meningitis
322.2	Chronic meningitis
322.9	Meningitis, unspecified
323	Encephalitis, myelitis, and encephalomyelitis
Includes:	acute disseminated encephalomyelitis
meningoencephalitis, except bacterial
meningomyelitis, except bacterial
myelitis:
ascending
transverse
Excludes:	acute transverse myelitis NOS (341.20)
acute transverse myelitis in conditions classified elsewhere (341.21)
bacterial:
meningoencephalitis (320.0-320.9)
meningomyelitis (320.0-320.9)
idiopathic transverse myelitis (341.22)
323.0	Encephalitis, myelitis, and encephalomyelitis in viral diseases classified
 elsewhere
Code first underlying disease, as:
cat-scratch disease (078.3)
infectious mononucleosis (075)
ornithosis (073.7)
323.01	Encephalitis and encephalomyelitis in viral diseases classified elsewhere
Excludes:	encephalitis (in):
arthropod-borne viral (062.0-064)
herpes simplex (054.3)
mumps (072.2)
other viral diseases of central nervous system (049.8-049.9)
poliomyelitis (045.0-045.9)
rubella (056.01)
slow virus infections of central nervous system (046.0-046.9)
viral NOS (049.9)
West Nile (066.41)
323.02	Myelitis in viral diseases classified elsewhere
Excludes:	myelitis (in):
herpes simplex (054.74)
herpes zoster (053.14)
other viral diseases of central nervous system (049.8-049.9)
poliomyelitis (045.0-045.9)
rubella (056.01)
323.1	Encephalitis, myelitis, and encephalomyelitis in rickettsial diseases classified
 elsewhere
Code first underlying disease (080-083.9)
323.2	Encephalitis, myelitis, and encephalomyelitis in protozoal diseases classified
 elsewhere
Code first underlying disease, as:
malaria (084.0-084.9)
trypanosomiasis (086.0-086.9)
323.4	Other encephalitis, myelitis, and encephalomyelitis due to infection classified
 elsewhere
Code first underlying disease
323.41	Other encephalitis and encephalomyelitis due to infection classified elsewhere
Excludes:	encephalitis (in):
meningococcal (036.1)
syphilis:
NOS (094.81)
congenital (090.41)
toxoplasmosis (130.0)
tuberculosis (013.6)
meningoencephalitis due to free-living ameba [Naegleria] (136.2)
323.42	Other myelitis due to infection classified elsewhere
Excludes:	myelitis (in):
syphilis (094.89)
tuberculosis (013.6)
323.5	Encephalitis, myelitis, and encephalomyelitis following immunization procedures
Use additional E code to identify vaccine
323.51	Encephalitis and encephalomyelitis following immunization procedures
Encephalitis postimmunization or postvaccinal
Encephalomyelitis postimmunization or postvaccinal
323.52	Myelitis following immunization procedures
Myelitis postimmunization or postvaccinal
323.6	Postinfectious encephalitis, myelitis, and encephalomyelitis
Code first underlying disease
323.61	Infectious acute disseminated encephalomyelitis (ADEM)
Acute necrotizing hemorrhagic encephalopathy
Excludes:noninfectious acute disseminated encephalomyelitis (323.81)
323.62	Other postinfectious encephalitis and encephalomyelitis
Excludes:	encephalitis:
postchickenpox (052.0)
postmeasles (055.0)
323.63	Postinfectious myelitis
323.7	Toxic encephalitis, myelitis, and encephalomyelitis
Code first underlying cause, as:
carbon tetrachloride (982.1)
hydroxyquinoline derivatives (961.3)
lead (984.0-984.9)
mercury (985.0)
thallium (985.8)
323.71	Toxic encephalitis and encephalomyelitis
323.72	Toxic myelitis
323.8	Other causes of encephalitis, myelitis, and encephalomyelitis
323.81	Other causes of encephalitis and encephalomyelitis
Noninfectious acute disseminated encephalomyelitis (ADEM)
323.82	Other causes of myelitis
Transverse myelitis NOS
323.9	Unspecified cause of encephalitis, myelitis, and encephalomyelitis
324	Intracranial and intraspinal abscess
324.0	Intracranial abscess
Abscess (embolic):
cerebellar
cerebral
Abscess (embolic) of brain [any part]:
epidural
extradural
otogenic
subdural
Excludes:	tuberculous (013.3)
324.1	Intraspinal abscess
Abscess (embolic) of spinal cord [any part]:
epidural
extradural
subdural
Excludes:	tuberculous (013.5)
324.9	Of unspecified site
Extradural or subdural abscess NOS
325	Phlebitis and thrombophlebitis of intracranial venous sinuses
Embolism of cavernous, lateral, or other intracranial or unspecified intracranial venous
 sinus
Endophlebitis of cavernous, lateral, or other intracranial or unspecified intracranial
 venous sinus
Phlebitis, septic or suppurative of cavernous, lateral, or other intracranial or
 unspecified intracranial venous sinus
Thrombophlebitis of cavernous, lateral, or other intracranial or unspecified
 intracranial venous sinus
Thrombosis of cavernous, lateral, or other intracranial or unspecified intracranial
 venous sinus
Excludes:	that specified as:
complicating pregnancy, childbirth, or the puerperium (671.5)
of nonpyogenic origin (437.6)
326	Late effects of intracranial abscess or pyogenic infection
Note:	This category is to be used to indicate conditions whose primary classification
 is to 320-325 [excluding 320.7, 321.0-321.8, 323.01-323.42, 323.61-323.72] as the cause
 of late effects, themselves classifiable elsewhere. The "late effects" include conditions
 specified as such, or as sequelae, which may occur at any time after the resolution of
 the causal condition.
Use additional code to identify condition, as:
hydrocephalus (331.4)
paralysis (342.0-342.9, 344.0-344.9)
ORGANIC SLEEP DISORDERS (327)
327	Organic sleep disorders
327.0	Organic disorders of initiating and maintaining sleep [Organic insomnia]
Excludes:	insomnia NOS (780.52)
insomnia not due to a substance or known physiological condition (307.41-307.42)
insomnia with sleep apnea NOS (780.51)
327.00	Organic insomnia, unspecified
327.01	Insomnia due to medical condition classified elsewhere
Code first underlying condition
Excludes:	insomnia due to mental disorder (327.02)
327.02	Insomnia due to mental disorder
Code first mental disorder
Excludes:	alcohol induced insomnia (291.82)
drug induced insomnia (292.85)
327.09	Other organic insomnia
327.1	Organic disorder of excessive somnolence [Organic hypersomnia]
Excludes:	hypersomnia NOS (780.54)
hypersomnia not due to a substance or known physiological condition (307.43-307.44)
hypersomnia with sleep apnea NOS (780.53)
327.10	Organic hypersomnia, unspecified
327.11	Idiopathic hypersomnia with long sleep time
327.12	Idiopathic hypersomnia without long sleep time
327.13	Recurrent hypersomnia
Kleine-Levin syndrome
Menstrual related hypersomnia
327.14	Hypersomnia due to medical condition classified elsewhere
Code first underlying condition
Excludes:	hypersomnia due to mental disorder (327.15)
327.15	Hypersomnia due to mental disorder
Code first mental disorder
Excludes:	alcohol induced insomnia (291.82)
drug induced insomnia (292.85)
327.19	Other organic hypersomnia
327.2	Organic sleep apnea
Excludes:	Cheyne-Stokes breathing (786.04)
hypersomnia with sleep apnea NOS (780.53)
insomnia with sleep apnea NOS (780.51)
sleep apnea in newborn  (770.81-770.82)
sleep apnea NOS (780.57)
327.20	Organic sleep apnea, unspecified
327.21	Primary central sleep apnea
327.22	High altitude periodic breathing
327.23	Obstructive sleep apnea (adult) (pediatric)
327.24	Idiopathic sleep related nonobstructive alveolar hypoventilation
Sleep related hypoxia
327.25	Congenital central alveolar hypoventilation syndrome
327.26	Sleep related hypoventilation/hypoxemia in conditions classifiable elsewhere
Code first underlying condition
327.27	Central sleep apnea in conditions classified elsewhere
Code first underlying condition
327.29	Other organic sleep apnea
327.3	Circadian rhythm sleep disorder
Organic disorder of sleep wake cycle
Organic disorder of sleep wake schedule
Excludes:	alcohol induced circadian rhythm sleep disorder (291.82)
circadian rhythm sleep disorder of nonorganic origin (307.45) 
disruption of 24 hour sleep wake cycle NOS (780.55)
drug induced circadian rhythm sleep disorder (292.85)
327.30	Circadian rhythm sleep disorder, unspecified
327.31	Circadian rhythm sleep disorder, delayed sleep phase type
327.32	Circadian rhythm sleep disorder, advanced sleep phase type
327.33	Circadian rhythm sleep disorder, irregular sleep-wake type
327.34	Circadian rhythm sleep disorder, free-running type
327.35	Circadian rhythm sleep disorder, jet lag type
327.36	Circadian rhythm sleep disorder, shift work type
327.37	Circadian rhythm sleep disorder in conditions classified elsewhere
Code first underlying condition
327.39	Other circadian rhythm sleep disorder
327.4	Organic parasomnia
Excludes:	alcohol induced parasomnia (291.82)
drug induced parasomnia (292.85)
parasomnia not due to a known physiological condition (307.47)
327.40	Organic parasomnia, unspecified
327.41	Confusional arousals
327.42	REM sleep behavior disorder
327.43	Recurrent isolated sleep paralysis
327.44	Parasomnia in conditions classified elsewhere
Code first underlying condition
327.49	Other organic parasomnia
327.5	Organic sleep related movement disorders
Excludes:	restless legs syndrome (333.94)
sleep related movement disorder NOS (780.58)
327.51	Periodic limb movement disorder
Periodic limb movement sleep disorder
327.52	Sleep related leg cramps
327.53	Sleep related bruxism
327.59	Other organic sleep related movement disorders
327.8	Other organic sleep disorders

HEREDITARY AND DEGENERATIVE DISEASES
   OF THE CENTRAL NERVOUS SYSTEM (330-337)

Excludes:	hepatolenticular degeneration (275.1)
multiple sclerosis (340)
other demyelinating diseases of central nervous system (341.0-341.9)
330	Cerebral degenerations usually manifest in childhood
Use additional code to identify associated mental retardation
330.0	Leukodystrophy
Krabbe's disease
Leukodystrophy:
NOS
globoid cell
metachromatic
sudanophilic
Pelizaeus-Merzbacher disease
Sulfatide lipidosis
330.1	Cerebral lipidoses
Amaurotic (familial) idiocy
Disease:
Batten
Jansky-Bielschowsky
Kufs'
Spielmeyer-Vogt
Tay-Sachs
Gangliosidosis
330.2	Cerebral degeneration in generalized lipidoses
Code first underlying disease, as:
Fabry's disease (272.7)
Gaucher's disease (272.7)
Niemann-Pick disease (272.7)
sphingolipidosis (272.7)
330.3	Cerebral degeneration of childhood in other diseases classified elsewhere
Code first underlying disease, as:
Hunter's disease (277.5)
mucopolysaccharidosis (277.5)
330.8	Other specified cerebral degenerations in childhood
Alpers' disease or gray-matter degeneration
Infantile necrotizing encephalomyelopathy
Leigh's disease
Subacute necrotizing encephalopathy or encephalomyelopathy
330.9	Unspecified cerebral degeneration in childhood
331	Other cerebral degenerations
Use additional code, where applicable, to identify:
with behavioral disturbance (294.11)
without behavioral disturbance (294.10)
331.0	Alzheimer's disease
331.1	Frontotemporal dementia
331.11	Pick's disease
331.19	Other frontotemporal dementia
Frontal dementia
331.2	Senile degeneration of brain
Excludes:	senility NOS (797)
331.3	Communicating hydrocephalus
Secondary normal pressure hydrocephalus
Excludes:	congenital hydrocephalus (742.3)
idiopathic normal pressure hydrocephalus (331.5)
normal pressure hydrocephalus (331.5)
spina bifida with hydrocephalus (741.0)
331.4	Obstructive hydrocephalus
Acquired hydrocephalus NOS
Excludes:	congenital hydrocephalus (742.3)
idiopathic normal pressure hydrocephalus (331.5)
normal pressure hydrocephalus (331.5)
spina bifida with hydrocephalus (741.0)
331.5	Idiopathic normal pressure hydrocephalus (INPH)
Normal pressure hydrocephalus NOS
Excludes:	congenital hydrocephalus (742.3)
secondary normal pressure hydrocephalus (331.3)
spina bifida with hydrocephalus (741.0)
331.7	Cerebral degeneration in diseases classified elsewhere
Code first underlying disease, as:
alcoholism (303.0-303.9)
beriberi (265.0)
cerebrovascular disease (430-438)
congenital hydrocephalus (741.0, 742.3)
neoplastic disease (140.0-239.9)
myxedema (244.0-244.9)
vitamin B12 deficiency (266.2)
Excludes:	cerebral degeneration in:
Jakob-Creutzfeldt disease (046.1)
progressive multifocal leukoencephalopathy (046.3)
subacute spongiform encephalopathy (046.1)
331.8	Other cerebral degeneration
331.81	Reye's syndrome
331.82	Dementia with Lewy bodies
Dementia with Parkinsonism
Lewy body dementia
Lewy body disease
331.83	Mild cognitive impairment, so stated
Excludes:	altered mental status (780.97)
cerebral degeneration (331.0-331.9)
change in mental status (780.97)
cognitive deficits following (late effects of) cerebral hemorrhage or infarction (438.0)
cognitive impairment due to intracranial or head injury (850-854, 959.01)
cognitive impairment due to late effect of intracranial injury (907.0)
dementia (290.0-290.43, 294.8)
mild memory disturbance (310.8)
neurologic neglect syndrome (781.8)
personality change, nonpsychotic (310.1)
331.89	Other
Cerebral ataxia
331.9	Cerebral degeneration, unspecified
332	Parkinson's disease
Excludes:	dementia with Parkinsonism (331.82)
332.0	Paralysis agitans
Parkinsonism or Parkinson's disease:
NOS
idiopathic
primary
332.1	Secondary Parkinsonism
Neuroleptic-induced Parkinsonism
Parkinsonism due to drugs
Use additional E code to identify drug, if drug-induced
Excludes:	Parkinsonism (in):
Huntington's disease (333.4)
progressive supranuclear palsy (333.0)
Shy-Drager syndrome (333.0)
syphilitic (094.82)
333	Other extrapyramidal disease and abnormal movement disorders
Includes:	other forms of extrapyramidal, basal ganglia, or striatopallidal disease
Excludes:	abnormal movements of head NOS (781.0)
sleep related movement disorders (327.51-327.59)
333.0	Other degenerative diseases of the basal ganglia
Atrophy or degeneration:
olivopontocerebellar [D�j�rine-Thomas syndrome]
pigmentary pallidal [Hallervorden-Spatz disease] striatonigral
Parkinsonian syndrome associated with:
idiopathic orthostatic hypotension
symptomatic orthostatic hypotension
Progressive supranuclear ophthalmoplegia
Shy-Drager syndrome
333.1	Essential and other specified forms of tremor
Benign essential tremor
Familial tremor
Medication-induced postural tremor
Use additional E code to identify drug, if drug-induced
Excludes:	tremor NOS (781.0)
333.2	Myoclonus
Familial essential myoclonus
Progressive myoclonic epilepsy
Unverricht-Lundborg disease
Use additional E code to identify drug, if drug-induced
333.3	Tics of organic origin
Excludes:	Gilles de la Tourette's syndrome (307.23)
habit spasm (307.22)
tic NOS (307.20)
Use additional E code to identify drug, if drug-induced
333.4	Huntington's chorea
333.5	Other choreas
Hemiballism(us)
Paroxysmal choreo-athetosis
Excludes:	Sydenham's or rheumatic chorea (392.0-392.9)
Use additional E code to identify drug, if drug-induced
333.6	Genetic torsion dystonia
Dystonia:
deformans progressiva
musculorum deformans
(Schwalbe-) Ziehen-Oppenheim disease
333.7	Acquired torsion dystonia
333.71	Athetoid cerebral palsy 
Double athetosis (syndrome)
Vogt's disease
Excludes:	infantile cerebral palsy (343.0-343.9)
333.72	Acute dystonia due to drugs
Acute dystonic reaction due to drugs
Neuroleptic-induced acute dystonia
Use additional E code to identify drug
Excludes:	blepharospasm due to drugs (333.85)
orofacial dyskinesia due to drugs (333.85)
secondary Parkinsonism (332.1)
subacute dyskinesia due to drugs (333.85)
tardive dyskinesia (333.85)
333.79	Other acquired torsion dystonia
333.8	Fragments of torsion dystonia
Use additional E code to identify drug, if drug-induced
333.81	Blepharospasm
Excludes:	blepharospasm due to drugs (333.85)
333.82	Orofacial dyskinesia
Excludes:	orofacial dyskinesia due to drugs (333.85)
333.83	Spasmodic torticollis
Excludes:	torticollis:
NOS (723.5)
hysterical (300.11)
psychogenic (306.0)
333.84	Organic writers' cramp
Excludes:	psychogenic (300.89)
333.85	Subacute dyskinesia due to drugs
Blepharospasm due to drugs
Orofacial dyskinesia due to drugs
Tardive dyskinesia
Use additional E code to identify drug
Excludes:	acute dystonia due to drugs (333.72)
acute dystonic reaction due to drugs (333.72)
secondary Parkinsonism (332.1)
333.89	Other
333.9	Other and unspecified extrapyramidal diseases and abnormal movement disorders
333.90	Unspecified extrapyramidal disease and abnormal movement disorder
Medication-induced movement disorders NOS
Use additional E code to identify drug, if drug-induced
333.91	Stiff-man syndrome
333.92	Neuroleptic malignant syndrome
Use additional E to identify drug
Excludes:	neuroleptic induced Parkinsonism (332.1)
333.93	Benign shuddering attacks
333.94	Restless legs syndrome (RLS)
333.99	Other
Neuroleptic-induced acute akathisia
Use additional E code to identify drug, if drug-induced
334	Spinocerebellar disease
Excludes:	olivopontocerebellar degeneration (333.0)
peroneal muscular atrophy (356.1)
334.0	Friedreich's ataxia
334.1	Hereditary spastic paraplegia
334.2	Primary cerebellar degeneration
Cerebellar ataxia:
Marie's
Sanger-Brown
Dyssynergia cerebellaris myoclonica
Primary cerebellar degeneration:
NOS
hereditary
sporadic
334.3	Other cerebellar ataxia
Cerebellar ataxia NOS
Use additional E code to identify drug, if drug-induced
334.4	Cerebellar ataxia in diseases classified elsewhere
Code first underlying disease, as:
alcoholism (303.0-303.9)
myxedema (244.0-244.9)
neoplastic disease (140.0-239.9)
334.8	Other spinocerebellar diseases
Ataxia-telangiectasia [Louis-Bar syndrome]
Corticostriatal-spinal degeneration
334.9	Spinocerebellar disease, unspecified
335	Anterior horn cell disease
335.0	Werdnig-Hoffmann disease
Infantile spinal muscular atrophy
Progressive muscular atrophy of infancy
335.1	Spinal muscular atrophy
335.10	Spinal muscular atrophy, unspecified
335.11	Kugelberg-Welander disease
Spinal muscular atrophy:
familial
juvenile
335.19	Other
Adult spinal muscular atrophy
335.2	Motor neuron disease
335.20	Amyotrophic lateral sclerosis
Motor neuron disease (bulbar) (mixed type)
335.21	Progressive muscular atrophy
Duchenne-Aran muscular atrophy
Progressive muscular atrophy (pure)
335.22	Progressive bulbar palsy
335.23	Pseudobulbar palsy
335.24	Primary lateral sclerosis
335.29	Other
335.8	Other anterior horn cell diseases
335.9	Anterior horn cell disease, unspecified
336	Other diseases of spinal cord
336.0	Syringomyelia and syringobulbia
336.1	Vascular myelopathies
Acute infarction of spinal cord (embolic) (nonembolic)
Arterial thrombosis of spinal cord
Edema of spinal cord
Hematomyelia
Subacute necrotic myelopathy
336.2	Subacute combined degeneration of spinal cord in diseases classified elsewhere
Code first underlying disease, as:
pernicious anemia (281.0)
other vitamin B12 deficiency anemia (281.1)
vitamin B12 deficiency (266.2)
336.3	Myelopathy in other diseases classified elsewhere
Code first underlying disease, as:
myelopathy in neoplastic disease (140.0-239.9)
Excludes:	myelopathy in:
intervertebral disc disorder (722.70-722.73)
spondylosis (721.1, 721.41-721.42, 721.91)
336.8	Other myelopathy
Myelopathy:
drug-induced
radiation-induced
Use additional E code to identify cause
336.9	Unspecified disease of spinal cord
Cord compression NOS
Myelopathy NOS
Excludes:	myelitis (323.02, 323.1, 323.2, 323.42, 323.52, 323.63, 323.72, 323.82, 323.9)
spinal (canal) stenosis (723.0, 724.00-724.09)
337	Disorders of the autonomic nervous system
Includes:	disorders of peripheral autonomic, sympathetic, parasympathetic, or
 vegetative system
Excludes:	familial dysautonomia [Riley-Day syndrome] (742.8)
337.0	Idiopathic peripheral autonomic neuropathy
Carotid sinus syncope or syndrome
Cervical sympathetic dystrophy or paralysis
337.1	Peripheral autonomic neuropathy in disorders classified elsewhere
Code first underlying disease, as:
amyloidosis (277.30-277.39)
diabetes (250.6)
337.2	Reflex sympathetic dystrophy
337.20	Reflex sympathetic dystrophy, unspecified
337.21	Reflex sympathetic dystrophy of the upper limb
337.22	Reflex sympathetic dystrophy of the lower limb
337.29	Reflex sympathetic dystrophy of other specified site
337.3	Autonomic dysreflexia
Use additional code to identify the cause, such as:
decubitus ulcer (707.00-707.09)
fecal impaction (560.39)
urinary tract infection (599.0)
337.9	Unspecified disorder of autonomic nervous system

PAIN (338)

338	Pain, not elsewhere classified
Use additional code to identify:
pain associated with psychological factors (307.89)
Excludes:	generalized pain (780.96)
localized pain, unspecified type - code to pain by site
pain disorder exclusively attributed to psychological factors (307.80)
338.0	Central pain syndrome
D�j�rine-Roussy syndrome
Myelopathic pain syndrome
Thalamic pain syndrome (hyperesthetic)
338.1	Acute pain
338.11	Acute pain due to trauma
338.12	Acute post-thoracotomy pain
Post-thoracotomy pain NOS
338.18	Other acute postoperative pain
Postoperative pain NOS
338.19	Other acute pain
Excludes:	neoplasm related acute pain (338.3)
338.2	Chronic pain
Excludes:	causalgia (355.9)
lower limb (355.71)
upper limb (354.4)
chronic pain syndrome (338.4)
myofascial pain syndrome (729.1)
neoplasm related chronic pain (338.3)
reflex sympathetic dystrophy (337.20-337.29)
338.21	Chronic pain due to trauma
338.22	Chronic post-thoracotomy pain
338.28	Other chronic postoperative pain
338.29	Other chronic pain
338.3	Neoplasm related pain (acute) (chronic)
Cancer associated pain
Pain due to malignancy (primary) (secondary)
Tumor associated pain
338.4	Chronic pain syndrome
Chronic pain associated with significant psychosocial dysfunction

OTHER DISORDERS OF THE CENTRAL NERVOUS SYSTEM (340-349)

340	Multiple sclerosis
Disseminated or multiple sclerosis:
NOS
brain stem
cord
generalized
341	Other demyelinating diseases of central nervous system
341.0	Neuromyelitis optica
341.1	Schilder's disease
Balo's concentric sclerosis
Encephalitis periaxialis:
concentrica [Balo's]
diffusa [Schilder's]
341.2	Acute (transverse) myelitis
Excludes:	acute (transverse) myelitis (in) (due to):
following immunization procedures (323.52)
infection classified elsewhere (323.42)
postinfectious (323.63)
protozoal diseases classified elsewhere (323.2)
rickettsial diseases classified elsewhere (323.1)
toxic (323.72)
viral diseases classified elsewhere (323.02)
transverse myelitis NOS (323.82)
341.20	Acute (transverse) myelitis NOS
341.21	Acute (transverse) myelitis in conditions classified elsewhere
Code first underlying condition
341.22	Idiopathic transverse myelitis
341.8	Other demyelinating diseases of central nervous system
Central demyelination of corpus callosum
Central pontine myelinosis
Marchiafava (-Bignami) disease
341.9	Demyelinating disease of central nervous system, unspecified
342	Hemiplegia and hemiparesis
Note:	This category is to be used when hemiplegia (complete) (incomplete) is reported
 without further specification, or is stated to be old or long-standing but of unspecified
 cause.  The category is also for use in multiple coding to identify these types of
 hemiplegia resulting from any cause.
Excludes:	congenital (343.1)
hemiplegia due to late effect of cerebrovascular accident (438.20-438.22)
infantile NOS (343.4)
The following fifth-digits are for use with codes 342.0-342.9
0	affecting unspecified side
1	affecting dominant side
2	affecting nondominant side
342.0	Flaccid hemiplegia
342.1	Spastic hemiplegia
342.8	Other specified hemiplegia
342.9	Hemiplegia, unspecified
343	Infantile cerebral palsy
Includes:	cerebral:
palsy NOS
spastic infantile paralysis
congenital spastic paralysis (cerebral)
Little's disease
paralysis (spastic) due to birth injury:
intracranial
spinal
Excludes:	athetoid cerebral palsy (333.71)
hereditary cerebral paralysis, such as:
hereditary spastic paraplegia (334.1)
Vogt's disease (333.71)
spastic paralysis specified as noncongenital or noninfantile (344.0-344.9)
343.0	Diplegic
Congenital diplegia
Congenital paraplegia
343.1	Hemiplegic
Congenital hemiplegia
Excludes:	infantile hemiplegia NOS (343.4)
343.2	Quadriplegic
Tetraplegic
343.3	Monoplegic
343.4	Infantile hemiplegia
Infantile hemiplegia (postnatal) NOS
343.8	Other specified infantile cerebral palsy
343.9	Infantile cerebral palsy, unspecified
Cerebral palsy NOS
344	Other paralytic syndromes
Note:	This category is to be used when the listed conditions are reported without
 further specification or are stated to be old or long-standing but of unspecified 
cause. The category is also for use in multiple coding to identify these conditions
 resulting from any cause.
Includes:	paralysis (complete) (incomplete), except as classifiable to 342 and 343
Excludes:	congenital or infantile cerebral palsy (343.0-343.9)
hemiplegia (342.0-342.9)
congenital or infantile (343.1, 343.4)
344.0	Quadriplegia and quadriparesis
344.00	Quadriplegia, unspecified
344.01	C1-C4, complete
344.02	C1-C4, incomplete
344.03	C5-C7, complete
344.04	C5-C7, incomplete
344.09	Other
344.1	Paraplegia
Paralysis of both lower limbs
Paraplegia (lower)
344.2	Diplegia of upper limbs
Diplegia (upper)
Paralysis of both upper limbs
344.3	Monoplegia of lower limb
Paralysis of lower limb
Excludes:	monoplegia of lower limb due to late effect of cerebrovascular
 accident (438.40-438.42)
344.30	Affecting unspecified side
344.31	Affecting dominant side
344.32	Affecting nondominant side
344.4	Monoplegia of upper limb
Paralysis of upper limb
Excludes:	monoplegia of upper limb due to late effect of cerebrovascular
 accident (438.30-438.32)
344.40	Affecting unspecified side
344.41	Affecting dominant side
344.42	Affecting nondominant side
344.5	Unspecified monoplegia
344.6	Cauda equina syndrome
344.60	Without mention of neurogenic bladder
344.61	With neurogenic bladder
Acontractile bladder
Autonomic hyperreflexia of bladder
Cord bladder
Detrusor hyperreflexia
344.8	Other specified paralytic syndromes
344.81	Locked-in state
344.89	Other specified paralytic syndrome
344.9	Paralysis, unspecified
345	Epilepsy and recurrent seizures
The following fifth-digit subclassification is for use with categories 345.0, .1, .4-.9:
0	without mention of intractable epilepsy
1	with intractable epilepsy
Excludes:	progressive myoclonic epilepsy (333.2)
345.0	Generalized nonconvulsive epilepsy
Absences:
atonic
typical
Minor epilepsy
Petit mal
Pykno-epilepsy
Seizures:
akinetic
atonic
345.1	Generalized convulsive epilepsy
Epileptic seizures:
clonic
myoclonic
tonic
tonic-clonic
Grand mal
Major epilepsy
Excludes:	convulsions:
NOS (780.39)
infantile (780.39)
newborn (779.0)
infantile spasms (345.6)
345.2	Petit mal status
Epileptic absence status
345.3	Grand mal status
Status epilepticus NOS
Excludes:	epilepsia partialis continua (345.7) status:
psychomotor (345.7)
temporal lobe (345.7)
345.4	Localization-related (focal) (partial) epilepsy and epileptic syndromes with
 complex partial seizures
Epilepsy:
limbic system
partial:
secondarily generalized
with impairment of consciousness
with memory and ideational disturbances
psychomotor
psychosensory
temporal lobe
Epileptic automatism
345.5	Localization-related (focal) (partial) epilepsy and epileptic syndromes with
 simple partial seizures
Epilepsy:
Bravais-Jacksonian NOS
focal (motor) NOS
Jacksonian NOS
motor partial
partial NOS
without mention of impairment of consciousness
sensory-induced
somatomotor
somatosensory
visceral
visual
345.6	Infantile spasms
Hypsarrhythmia
Lightning spasms
Salaam attacks
Excludes:	salaam tic (781.0)
345.7	Epilepsia partialis continua
Kojevnikov's epilepsy
345.8	Other forms of epilepsy and recurrent seizures
Epilepsy:
cursive [running]
gelastic
Recurrent seizures NOS
Seizure disorder NOS
345.9	Epilepsy, unspecified
Epileptic convulsions, fits, or seizures NOS
Recurrent seizures NOS
Seizure disorder NOS
Excludes:	convulsion (convulsive) disorder (780.39)
convulsive seizure or fit NOS (780.39)
recurrent convulsions (780.39)
346	Migraine
The following fifth-digit subclassification is for use with category 346:
0	without mention of intractable migraine
1	with intractable migraine, so stated
346.0	Classical migraine
Migraine preceded or accompanied by transient focal neurological phenomena
Migraine with aura
346.1	Common migraine
Atypical migraine
Sick headache
346.2	Variants of migraine
Cluster headache
Histamine cephalgia
Horton's neuralgia
Migraine:
abdominal
basilar
lower half
retinal
Neuralgia:
ciliary
migrainous
346.8	Other forms of migraine
Migraine:
hemiplegic
ophthalmoplegic
346.9	Migraine, unspecified
347	Cataplexy and narcolepsy
347.0	Narcolepsy
347.00	Without cataplexy
Narcolepsy NOS
347.01	With cataplexy
347.1	Narcolepsy in conditions classified elsewhere
Code first underlying condition
347.10	Without cataplexy
347.11	With cataplexy	
348	Other conditions of brain
348.0	Cerebral cysts
Arachnoid cyst
Porencephalic cyst
Porencephaly, acquired
Pseudoporencephaly
348.1	Anoxic brain damage
Excludes:	that occurring in:
abortion (634-638 with .7, 639.8)
ectopic or molar pregnancy (639.8)
labor or delivery (668.2, 669.4)
that of newborn (767.0, 768.0-768.9, 772.1-772.2)
Use additional E code to identify cause
348.2	Benign intracranial hypertension
Pseudotumor cerebri
Excludes:	hypertensive encephalopathy (437.2)
348.3	Encephalopathy, not elsewhere classified
348.30	Encephalopathy, unspecified
348.31	Metabolic encephalopathy
Septic encephalopathy
Excludes:	toxic metabolic encephalopathy (349.82)
348.39	Other encephalopathy
Excludes:	encephalopathy:
alcoholic (291.2)
hepatic (572.2)
hypertensive (437.2)
toxic (349.82)
348.4	Compression of brain
Compression brain (stem)
Herniation brain (stem)
Posterior fossa compression syndrome
348.5	Cerebral edema
348.8	Other conditions of brain
Cerebral:
calcification
fungus
348.9	Unspecified condition of brain
349	Other and unspecified disorders of the nervous system
349.0	Reaction to spinal or lumbar puncture
Headache following lumbar puncture
349.1	Nervous system complications from surgically implanted device
Excludes:	immediate postoperative complications (997.00-997.09)
mechanical complications of nervous system device (996.2)
349.2	Disorders of meninges, not elsewhere classified
Adhesions, meningeal (cerebral) (spinal)
Cyst, spinal meninges
Meningocele, acquired
Pseudomeningocele, acquired
349.8	Other specified disorders of nervous system
349.81	Cerebrospinal fluid rhinorrhea
Excludes:	cerebrospinal fluid otorrhea (388.61)
349.82	Toxic encephalopathy
Toxic metabolic encephalopathy
Use additional E code to identify cause
349.89	Other
349.9	Unspecified disorders of nervous system
Disorder of nervous system (central) NOS

DISORDERS OF THE PERIPHERAL NERVOUS SYSTEM (350-359)

Excludes:	diseases of:
acoustic [8th] nerve (388.5)
oculomotor [3rd, 4th, 6th] nerves (378.0-378.9)
optic [2nd] nerve (377.0-377.9)
peripheral autonomic nerves (337.0-337.9)
neuralgia NOS or "rheumatic" (729.2)
neuritis NOS or "rheumatic" (729.2)
radiculitis NOS or "rheumatic" (729.2)
peripheral neuritis in pregnancy (646.4)
350	Trigeminal nerve disorders
Includes:	disorders of 5th cranial nerve
350.1	Trigeminal neuralgia
Tic douloureux
Trifacial neuralgia
Trigeminal neuralgia NOS
Excludes:	postherpetic (053.12)
350.2	Atypical face pain
350.8	Other specified trigeminal nerve disorders
350.9	Trigeminal nerve disorder, unspecified
351	Facial nerve disorders
Includes:	disorders of 7th cranial nerve
Excludes:	that in newborn (767.5)
351.0	Bell's palsy
Facial palsy
351.1	Geniculate ganglionitis
Geniculate ganglionitis NOS
Excludes:	herpetic (053.11)
351.8	Other facial nerve disorders
Facial myokymia
Melkersson's syndrome
351.9	Facial nerve disorder, unspecified
352	Disorders of other cranial nerves
352.0	Disorders of olfactory [1st] nerve
352.1	Glossopharyngeal neuralgia
352.2	Other disorders of glossopharyngeal [9th] nerve
352.3	Disorders of pneumogastric [10th] nerve
Disorders of vagal nerve
Excludes:	paralysis of vocal cords or larynx (478.30-478.34)
352.4	Disorders of accessory [11th] nerve
352.5	Disorders of hypoglossal [12th] nerve
352.6	Multiple cranial nerve palsies
Collet-Sicard syndrome
Polyneuritis cranialis
352.9	Unspecified disorder of cranial nerves
353	Nerve root and plexus disorders
Excludes:	conditions due to:
intervertebral disc disorders (722.0-722.9)
spondylosis (720.0-721.9)
vertebrogenic disorders (723.0-724.9)
353.0	Brachial plexus lesions
Cervical rib syndrome
Costoclavicular syndrome
Scalenus anticus syndrome
Thoracic outlet syndrome
Excludes:	brachial neuritis or radiculitis NOS (723.4)
that in newborn (767.6)
353.1	Lumbosacral plexus lesions
Code first, if applicable, associated diabetes mellitus (250.6)
353.2	Cervical root lesions, not elsewhere classified
353.3	Thoracic root lesions, not elsewhere classified
353.4	Lumbosacral root lesions, not elsewhere classified
353.5	Neuralgic amyotrophy
Parsonage-Aldren-Turner syndrome
353.6	Phantom limb (syndrome)
353.8	Other nerve root and plexus disorders
353.9	Unspecified nerve root and plexus disorder
354	Mononeuritis of upper limb and mononeuritis multiplex
354.0	Carpal tunnel syndrome
Median nerve entrapment
Partial thenar atrophy
354.1	Other lesion of median nerve
Median nerve neuritis
354.2	Lesion of ulnar nerve
Cubital tunnel syndrome
Tardy ulnar nerve palsy
354.3	Lesion of radial nerve
Acute radial nerve palsy
354.4	Causalgia of upper limb
Excludes:	causalgia:
NOS (355.9)
lower limb (355.71)
354.5	Mononeuritis multiplex
Combinations of single conditions classifiable to 354 or 355
354.8	Other mononeuritis of upper limb
354.9	Mononeuritis of upper limb, unspecified
355	Mononeuritis of lower limb
355.0	Lesion of sciatic nerve
Excludes:	sciatica NOS (724.3)
355.1	Meralgia paresthetica
Lateral cutaneous femoral nerve of thigh compression or syndrome
355.2	Other lesion of femoral nerve
355.3	Lesion of lateral popliteal nerve
Lesion of common peroneal nerve
355.4	Lesion of medial popliteal nerve
355.5	Tarsal tunnel syndrome
355.6	Lesion of plantar nerve
Morton's metatarsalgia, neuralgia, or neuroma
355.7	Other mononeuritis of lower limb
355.71	Causalgia of lower limb
Excludes:	causalgia:
NOS (355.9)
upper limb (354.4)
355.79	Other mononeuritis of lower limb
355.8	Mononeuritis of lower limb, unspecified
355.9	Mononeuritis of unspecified site
Causalgia NOS
Excludes:	causalgia:
lower limb (355.71)
upper limb (354.4)
356	Hereditary and idiopathic peripheral neuropathy
356.0	Hereditary peripheral neuropathy
D�j�rine-Sottas disease
356.1	Peroneal muscular atrophy
Charcot-Marie-Tooth disease
Neuropathic muscular atrophy
356.2	Hereditary sensory neuropathy
356.3	Refsum's disease
Heredopathia atactica polyneuritiformis
356.4	Idiopathic progressive polyneuropathy
356.8	Other specified idiopathic peripheral neuropathy
Supranuclear paralysis
356.9	Unspecified
357	Inflammatory and toxic neuropathy
357.0	Acute infective polyneuritis
Guillain-Barre syndrome
Postinfectious polyneuritis
357.1	Polyneuropathy in collagen vascular disease
Code first underlying disease, as:
disseminated lupus erythematosus (710.0)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
357.2	Polyneuropathy in diabetes
Code first underlying disease (250.6)
357.3	Polyneuropathy in malignant disease
Code first underlying disease (140.0-208.9)
357.4	Polyneuropathy in other diseases classified elsewhere
Code first underlying disease, as:
amyloidosis (277.30-277.39)
beriberi (265.0)
chronic uremia (585.9)
deficiency of B vitamins (266.0-266.9)
diphtheria (032.0-032.9)
hypoglycemia (251.2)
pellagra (265.2)
porphyria (277.1)
sarcoidosis (135)
uremia NOS (586)
Excludes:	polyneuropathy in:
herpes zoster (053.13)
mumps (072.72)
357.5	Alcoholic polyneuropathy
357.6	Polyneuropathy due to drugs
Use additional E code to identify drug
357.7	Polyneuropathy due to other toxic agents
Use additional E code to identify toxic agent
357.8	Other
357.81	Chronic inflammatory demyelinating polyneuritis
357.82	Critical illness polyneuropathy
Acute motor neuropathy
357.89	Other inflammatory and toxic neuropathy
357.9	Unspecified
358	Myoneural disorders
358.0	Myasthenia gravis
358.00	Myasthenia gravis without (acute) exacerbation
358.01	Myasthenia gravis with (acute) exacerbation
Myasthenia gravis in crisis
358.1	Myasthenic syndromes in diseases classified elsewhere
Eaton-Lambert syndrome from stated cause classified elsewhere
Code first underlying disease, as:
botulism (005.1)
hypothyroidism (244.0-244.9)
malignant neoplasm (140.0-208.9)
pernicious anemia (281.0)
thyrotoxicosis (242.0-242.9)
358.2	Toxic myoneural disorders
Use additional E code to identify toxic agent
358.8	Other specified myoneural disorders
358.9	Myoneural disorders, unspecified
359	Muscular dystrophies and other myopathies
Excludes:	idiopathic polymyositis (710.4)
359.0	Congenital hereditary muscular dystrophy
Benign congenital myopathy
Central core disease
Centronuclear myopathy
Myotubular myopathy
Nemaline body disease
Excludes:	arthrogryposis multiplex congenita (754.89)
359.1	Hereditary progressive muscular dystrophy
Muscular dystrophy:
NOS
distal
Duchenne
Erb's
fascioscapulohumeral
Gower's
Landouzy-D�j�rine
limb-girdle
ocular
oculopharyngeal
359.2	Myotonic disorders
Excludes:	periodic paralysis (359.3)
359.21	Myotonic muscular dystrophy
Dystrophia myotonica
Myotonia atrophica
Myotonic dystrophy
Proximal myotonic myopathy (PROMM)
Steinert's disease
359.22	Myotonia congenita
Acetazolamide responsive myotonia congenita
Dominant form (Thomsen's disease)
Recessive form (Becker's disease)
359.23	Myotonic chondrodystrophy
Congenital myotonic chondrodystrophy
Schwartz-Jampel disease
359.24	Drug-induced myotonia
Use additional E code to identify drug
359.29	Other specified myotonic disorder
Myotonia fluctuans
Myotonia levior
Myotonia permanens
Paramyotonia congenita (of von Eulenburg)
359.3	Periodic paralysis
Familial periodic paralysis
Hyperkalemic periodic paralysis
Hypokalemic familial periodic paralysis
Hypokalemic periodic paralysis
Potassium sensitive periodic paralysis
Excludes:	paramyotonia congenita (of von Eulenburg) (359.29)
359.4	Toxic myopathy
Use additional E code to identify toxic agent
359.5	Myopathy in endocrine diseases classified elsewhere
Code first underlying disease, as:
Addison's disease (255.41)
Cushing's syndrome (255.0)
hypopituitarism (253.2)
myxedema (244.0-244.9)
thyrotoxicosis (242.0-242.9)
359.6	Symptomatic inflammatory myopathy in diseases classified elsewhere
Code first underlying disease, as:
amyloidosis (277.30-277.39)
disseminated lupus erythematosus (710.0)
malignant neoplasm (140.0-208.9)
polyarteritis nodosa (446.0)
rheumatoid arthritis (714.0)
sarcoidosis (135)
scleroderma (710.1)
Sj�gren's disease (710.2)
359.8	Other myopathies
359.81	Critical illness myopathy
Acute necrotizing myopathy
Acute quadriplegic myopathy
Intensive care (ICU) myopathy
Myopathy of critical illness
359.89	Other myopathies
359.9	Myopathy, unspecified

DISORDERS OF THE EYE AND ADNEXA (360-379)

360	Disorders of the globe
Includes:	disorders affecting multiple structures of eye
360.0	Purulent endophthalmitis
Excludes:	bleb associated endophthalmitis (379.63)
360.00	Purulent endophthalmitis, unspecified
360.01	Acute endophthalmitis
360.02	Panophthalmitis
360.03	Chronic endophthalmitis
360.04	Vitreous abscess
360.1	Other endophthalmitis
Excludes:	bleb associated endophthalmitis (379.63)
360.11	Sympathetic uveitis
360.12	Panuveitis
360.13	Parasitic endophthalmitis NOS
360.14	Ophthalmia nodosa
360.19	Other
Phacoanaphylactic endophthalmitis
360.2	Degenerative disorders of globe
360.20	Degenerative disorder of globe, unspecified
360.21	Progressive high (degenerative) myopia
Malignant myopia
360.23	Siderosis
360.24	Other metallosis
Chalcosis
360.29	Other
Excludes:	xerophthalmia (264.7)
360.3	Hypotony of eye
360.30	Hypotony, unspecified
360.31	Primary hypotony
360.32	Ocular fistula causing hypotony
360.33	Hypotony associated with other ocular disorders
360.34	Flat anterior chamber
360.4	Degenerated conditions of globe
360.40	Degenerated globe or eye, unspecified
360.41	Blind hypotensive eye
Atrophy of globe
Phthisis bulbi
360.42	Blind hypertensive eye
Absolute glaucoma
360.43	Hemophthalmos, except current injury
Excludes:	traumatic (871.0-871.9, 921.0-921.9)
360.44	Leucocoria
360.5	Retained (old) intraocular foreign body, magnetic
Excludes:	current penetrating injury with magnetic foreign body (871.5)
retained (old) foreign body of orbit (376.6)
360.50	Foreign body, magnetic, intraocular, unspecified
360.51	Foreign body, magnetic, in anterior chamber
360.52	Foreign body, magnetic, in iris or ciliary body
360.53	Foreign body, magnetic, in lens
360.54	Foreign body, magnetic, in vitreous
360.55	Foreign body, magnetic, in posterior wall
360.59	Foreign body, magnetic, in other or multiple sites
360.6	Retained (old) intraocular foreign body, nonmagnetic
Retained (old) foreign body:
NOS
nonmagnetic
Excludes:	current penetrating injury with (nonmagnetic) foreign body (871.6)
retained (old) foreign body in orbit (376.6)
360.60	Foreign body, intraocular, unspecified
360.61	Foreign body in anterior chamber
360.62	Foreign body in iris or ciliary body
360.63	Foreign body in lens
360.64	Foreign body in vitreous
360.65	Foreign body in posterior wall
360.69	Foreign body in other or multiple sites
360.8	Other disorders of globe
360.81	Luxation of globe
360.89	Other
360.9	Unspecified disorder of globe
361	Retinal detachments and defects
361.0	Retinal detachment with retinal defect
Rhegmatogenous retinal detachment
Excludes:	detachment of retinal pigment epithelium (362.42-362.43)
retinal detachment (serous) (without defect) (361.2)
361.00	Retinal detachment with retinal defect, unspecified
361.01	Recent detachment, partial, with single defect
361.02	Recent detachment, partial, with multiple defects
361.03	Recent detachment, partial, with giant tear
361.04	Recent detachment, partial, with retinal dialysis
Dialysis (juvenile) of retina (with detachment)
361.05	Recent detachment, total or subtotal
361.06	Old detachment, partial
Delimited old retinal detachment
361.07	Old detachment, total or subtotal
361.1	Retinoschisis and retinal cysts
Excludes:	juvenile retinoschisis (362.73)
microcystoid degeneration of retina (362.62)
parasitic cyst of retina (360.13)
361.10	Retinoschisis, unspecified
361.11	Flat retinoschisis
361.12	Bullous retinoschisis
361.13	Primary retinal cysts
361.14	Secondary retinal cysts
361.19	Other
Pseudocyst of retina
361.2	Serous retinal detachment
Retinal detachment without retinal defect
Excludes:	central serous retinopathy (362.41)
retinal pigment epithelium detachment (362.42-362.43)
361.3	Retinal defects without detachment
Excludes:	chorioretinal scars after surgery for detachment (363.30-363.35)
peripheral retinal degeneration without defect (362.60-362.66)
361.30	Retinal defect, unspecified
Retinal break(s) NOS
361.31	Round hole of retina without detachment
361.32	Horseshoe tear of retina without detachment
Operculum of retina without mention of detachment
361.33	Multiple defects of retina without detachment
361.8	Other forms of retinal detachment
361.81	Traction detachment of retina
Traction detachment with vitreoretinal organization
361.89	Other
361.9	Unspecified retinal detachment
362	Other retinal disorders
Excludes:	chorioretinal scars (363.30-363.35)
chorioretinitis (363.0-363.2)
362.0	Diabetic retinopathy
Code first diabetes (250.5)
362.01	Background diabetic retinopathy
Diabetic retinal microaneurysms
Diabetic retinopathy NOS
362.02	Proliferative diabetic retinopathy
362.03	Nonproliferative diabetic retinopathy NOS
362.04	Mild nonproliferative diabetic retinopathy
362.05	Moderate nonproliferative diabetic retinopathy
362.06	Severe nonproliferative diabetic retinopathy
362.07	Diabetic macular edema
Diabetic retinal edema
Note: Code 362.07 must be used with a code for diabetic retinopathy (362.01-362.06)
362.1	Other background retinopathy and retinal vascular changes
362.10	Background retinopathy, unspecified
362.11	Hypertensive retinopathy
362.12	Exudative retinopathy
Coats' syndrome
362.13	Changes in vascular appearance
Vascular sheathing of retina
Use additional code for any associated atherosclerosis (440.8)
362.14	Retinal microaneurysms NOS
362.15	Retinal telangiectasia
362.16	Retinal neovascularization NOS
Neovascularization:
choroidal
subretinal
362.17	Other intraretinal microvascular abnormalities
Retinal varices
362.18	Retinal vasculitis
Eales' disease
Retinal:
arteritis
endarteritis
perivasculitis
phlebitis
362.2	Other proliferative retinopathy
362.21	Retrolental fibroplasia
362.29	Other nondiabetic proliferative retinopathy
362.3	Retinal vascular occlusion
362.30	Retinal vascular occlusion, unspecified
362.31	Central retinal artery occlusion
362.32	Arterial branch occlusion
362.33	Partial arterial occlusion
Hollenhorst plaque
Retinal microembolism
362.34	Transient arterial occlusion
Amaurosis fugax
362.35	Central retinal vein occlusion
362.36	Venous tributary (branch) occlusion
362.37	Venous engorgement
Occlusion:
of retinal vein
incipient of retinal vein
partial of retinal vein
362.4	Separation of retinal layers
Excludes:	retinal detachment (serous) (361.2)
rhegmatogenous (361.00-361.07)
362.40	Retinal layer separation, unspecified
362.41	Central serous retinopathy
362.42	Serous detachment of retinal pigment epithelium
Exudative detachment of retinal pigment epithelium
362.43	Hemorrhagic detachment of retinal pigment epithelium
362.5	Degeneration of macula and posterior pole
Excludes:	degeneration of optic disc (377.21-377.24)
hereditary retinal degeneration [dystrophy] (362.70-362.77)
362.50	Macular degeneration (senile), unspecified
362.51	Nonexudative senile macular degeneration
Senile macular degeneration:
atrophic
dry
362.52	Exudative senile macular degeneration
Kuhnt-Junius degeneration
Senile macular degeneration:
disciform
wet
362.53	Cystoid macular degeneration
Cystoid macular edema
362.54	Macular cyst, hole, or pseudohole
362.55	Toxic maculopathy
Use additional E to identify drug, if drug induced
362.56	Macular puckering
Preretinal fibrosis
362.57	Drusen (degenerative)
362.6	Peripheral retinal degenerations
Excludes:	hereditary retinal degeneration [dystrophy] (362.70-362.77)
retinal degeneration with retinal defect (361.00-361.07)
362.60	Peripheral retinal degeneration, unspecified
362.61	Paving stone degeneration
362.62	Microcystoid degeneration
Blessig's cysts
Iwanoff's cysts
362.63	Lattice degeneration
Palisade degeneration of retina
362.64	Senile reticular degeneration
362.65	Secondary pigmentary degeneration
Pseudoretinitis pigmentosa
362.66	Secondary vitreoretinal degenerations
362.7	Hereditary retinal dystrophies
362.70	Hereditary retinal dystrophy, unspecified
362.71	Retinal dystrophy in systemic or cerebroretinal lipidoses
Code first underlying disease, as:
cerebroretinal lipidoses (330.1)
systemic lipidoses (272.7)
362.72	Retinal dystrophy in other systemic disorders and syndromes
Code first underlying disease, as:
Bassen-Kornzweig syndrome (272.5)
Refsum's disease (356.3)
362.73	Vitreoretinal dystrophies
Juvenile retinoschisis
362.74	Pigmentary retinal dystrophy
Retinal dystrophy, albipunctate
Retinitis pigmentosa
362.75	Other dystrophies primarily involving the sensory retina
Progressive cone (-rod) dystrophy
Stargardt's disease
362.76	Dystrophies primarily involving the retinal pigment epithelium
Fundus flavimaculatus
Vitelliform dystrophy
362.77	Dystrophies primarily involving Bruch's membrane
Dystrophy:
hyaline
pseudoinflammatory foveal
Hereditary drusen
362.8	Other retinal disorders
Excludes:	chorioretinal inflammations (363.0-363.2)
chorioretinal scars (363.30-363.35)
362.81	Retinal hemorrhage
Hemorrhage:
preretinal
retinal (deep) (superficial)
subretinal
362.82	Retinal exudates and deposits
362.83	Retinal edema
Retinal:
cotton wool spots
edema (localized) (macular) (peripheral)
362.84	Retinal ischemia
362.85	Retinal nerve fiber bundle defects
362.89	Other retinal disorders
362.9	Unspecified retinal disorder
363	Chorioretinal inflammations, scars, and other disorders of choroid
363.0	Focal chorioretinitis and focal retinochoroiditis
Excludes:	focal chorioretinitis or retinochoroiditis in:
histoplasmosis (115.02, 115.12, 115.92)
toxoplasmosis (130.2)
congenital infection (771.2)
363.00	Focal chorioretinitis, unspecified
Focal:
choroiditis or chorioretinitis NOS
retinitis or retinochoroiditis NOS
363.01	Focal choroiditis and chorioretinitis, juxtapapillary
363.03	Focal choroiditis and chorioretinitis of other posterior pole
363.04	Focal choroiditis and chorioretinitis, peripheral
363.05	Focal retinitis and retinochoroiditis, juxtapapillary
Neuroretinitis
363.06	Focal retinitis and retinochoroiditis, macular or paramacular
363.07	Focal retinitis and retinochoroiditis of other posterior pole
363.08	Focal retinitis and retinochoroiditis, peripheral
363.1	Disseminated chorioretinitis and disseminated retinochoroiditis
Excludes:	disseminated choroiditis or chorioretinitis in secondary syphilis (091.51)
neurosyphilitic disseminated retinitis or retinochoroiditis (094.83)
retinal (peri)vasculitis (362.18)
363.10	Disseminated chorioretinitis, unspecified
Disseminated:
choroiditis or chorioretinitis NOS
retinitis or retinochoroiditis NOS
363.11	Disseminated choroiditis and chorioretinitis, posterior pole
363.12	Disseminated choroiditis and chorioretinitis, peripheral
363.13	Disseminated choroiditis and chorioretinitis, generalized
Code first any underlying disease, as:
tuberculosis (017.3)
363.14	Disseminated retinitis and retinochoroiditis, metastatic
363.15	Disseminated retinitis and retinochoroiditis, pigment epitheliopathy
Acute posterior multifocal placoid pigment epitheliopathy
363.2	Other and unspecified forms of chorioretinitis and retinochoroiditis
Excludes:	panophthalmitis (360.02)
sympathetic uveitis (360.11)
uveitis NOS (364.3)
363.20	Chorioretinitis, unspecified
Choroiditis NOS
Retinitis NOS
Uveitis, posterior NOS
363.21	Pars planitis
Posterior cyclitis
363.22	Harada's disease
363.3	Chorioretinal scars
Scar (postinflammatory) (postsurgical) (posttraumatic):
choroid
retina
363.30	Chorioretinal scar, unspecified
363.31	Solar retinopathy
363.32	Other macular scars
363.33	Other scars of posterior pole
363.34	Peripheral scars
363.35	Disseminated scars
363.4	Choroidal degenerations
363.40	Choroidal degeneration, unspecified
Choroidal sclerosis NOS
363.41	Senile atrophy of choroid
363.42	Diffuse secondary atrophy of choroid
363.43	Angioid streaks of choroid
363.5	Hereditary choroidal dystrophies
Hereditary choroidal atrophy:
partial [choriocapillaris]
total [all vessels]
363.50	Hereditary choroidal dystrophy or atrophy, unspecified
363.51	Circumpapillary dystrophy of choroid, partial
363.52	Circumpapillary dystrophy of choroid, total
Helicoid dystrophy of choroid
363.53	Central dystrophy of choroid, partial
Dystrophy, choroidal:
central areolar
circinate
363.54	Central choroidal atrophy, total
Dystrophy, choroidal:
central gyrate
serpiginous
363.55	Choroideremia
363.56	Other diffuse or generalized dystrophy, partial
Diffuse choroidal sclerosis
363.57	Other diffuse or generalized dystrophy, total
Generalized gyrate atrophy, choroid
363.6	Choroidal hemorrhage and rupture
363.61	Choroidal hemorrhage, unspecified
363.62	Expulsive choroidal hemorrhage
363.63	Choroidal rupture
363.7	Choroidal detachment
363.70	Choroidal detachment, unspecified
363.71	Serous choroidal detachment
363.72	Hemorrhagic choroidal detachment
363.8	Other disorders of choroid
363.9	Unspecified disorder of choroid
364	Disorders of iris and ciliary body
364.0	Acute and subacute iridocyclitis
Anterior uveitis, acute, subacute
Cyclitis, acute, subacute
Iridocyclitis, acute, subacute
Iritis, acute, subacute
Excludes:	gonococcal (098.41)
herpes simplex (054.44)
herpes zoster (053.22)
364.00	Acute and subacute iridocyclitis, unspecified
364.01	Primary iridocyclitis
364.02	Recurrent iridocyclitis
364.03	Secondary iridocyclitis, infectious
364.04	Secondary iridocyclitis, noninfectious
Aqueous:
cells
fibrin
flare
364.05	Hypopyon
364.1	Chronic iridocyclitis
Excludes:	posterior cyclitis (363.21)
364.10	Chronic iridocyclitis, unspecified
364.11	Chronic iridocyclitis in diseases classified elsewhere
Code first underlying disease, as:
sarcoidosis (135)
tuberculosis (017.3)
Excludes:	syphilitic iridocyclitis (091.52)
364.2	Certain types of iridocyclitis
Excludes:	posterior cyclitis (363.21)
sympathetic uveitis (360.11)
364.21	Fuchs' heterochromic cyclitis
364.22	Glaucomatocyclitic crises
364.23	Lens-induced iridocyclitis
364.24	Vogt-Koyanagi syndrome
364.3	Unspecified iridocyclitis
Uveitis NOS
364.4	Vascular disorders of iris and ciliary body
364.41	Hyphema
Hemorrhage of iris or ciliary body
364.42	Rubeosis iridis
Neovascularization of iris or ciliary body
364.5	Degenerations of iris and ciliary body
364.51	Essential or progressive iris atrophy
364.52	Iridoschisis
364.53	Pigmentary iris degeneration
Acquired heterochromia of iris
Pigment dispersion syndrome of iris
Translucency of iris
364.54	Degeneration of pupillary margin
Atrophy of sphincter of iris
Ectropion of pigment epithelium of iris
364.55	Miotic cysts of pupillary margin
364.56	Degenerative changes of chamber angle
364.57	Degenerative changes of ciliary body
364.59	Other iris atrophy
Iris atrophy (generalized) (sector shaped)
364.6	Cysts of iris, ciliary body, and anterior chamber
Excludes:	miotic pupillary cyst (364.55)
parasitic cyst (360.13)
364.60	Idiopathic cysts
364.61	Implantation cysts
Epithelial down-growth, anterior chamber
Implantation cysts (surgical) (traumatic)
364.62	Exudative cysts of iris or anterior chamber
364.63	Primary cyst of pars plana
364.64	Exudative cyst of pars plana
364.7	Adhesions and disruptions of iris and ciliary body
Excludes:	flat anterior chamber (360.34)
364.70	Adhesions of iris, unspecified
Synechiae (iris) NOS
364.71	Posterior synechiae
364.72	Anterior synechiae
364.73	Goniosynechiae
Peripheral anterior synechiae
364.74	Pupillary membranes
Iris bomb�
Pupillary:
occlusion
seclusion
364.75	Pupillary abnormalities
Deformed pupil
Ectopic pupil
Rupture of sphincter, pupil
364.76	Iridodialysis
364.77	Recession of chamber angle
364.8	Other disorders of iris and ciliary body
364.81	Floppy iris syndrome
Intraoperative floppy iris syndrome (IFIS)
Use additional E code to identify cause, such as:
sympatholytics [antiadrenergics] causing adverse effect in therapeutic use (E941.3)
364.89	Other disorders of iris and ciliary body
Prolapse of iris NOS
Excludes:	prolapse of iris in recent wound (871.1) 
364.9	Unspecified disorder of iris and ciliary body
365	Glaucoma
Excludes:	blind hypertensive eye [absolute glaucoma] (360.42)
congenital glaucoma (743.20-743.22)
365.0	Borderline glaucoma [glaucoma suspect]
365.00	Preglaucoma, unspecified
365.01	Open angle with borderline findings
Open angle with:
borderline intraocular pressure
cupping of optic discs
365.02	Anatomical narrow angle
365.03	Steroid responders
365.04	Ocular hypertension
365.1	Open-angle glaucoma
365.10	Open-angle glaucoma, unspecified
Wide-angle glaucoma NOS
365.11	Primary open angle glaucoma
Chronic simple glaucoma
365.12	Low tension glaucoma
365.13	Pigmentary glaucoma
365.14	Glaucoma of childhood
Infantile or juvenile glaucoma
365.15	Residual stage of open angle glaucoma
365.2	Primary angle-closure glaucoma
365.20	Primary angle-closure glaucoma, unspecified
365.21	Intermittent angle-closure glaucoma
Angle-closure glaucoma:
interval
subacute
365.22	Acute angle-closure glaucoma
365.23	Chronic angle-closure glaucoma
365.24	Residual stage of angle-closure glaucoma
365.3	Corticosteroid-induced glaucoma
365.31	Glaucomatous stage
365.32	Residual stage
365.4	Glaucoma associated with congenital anomalies, dystrophies, and systemic
 syndromes
365.41	Glaucoma associated with chamber angle anomalies
Code first associated disorder, as:
Axenfeld's anomaly (743.44)
Rieger's anomaly or syndrome (743.44)
365.42	Glaucoma associated with anomalies of iris
Code first associated disorder, as:
aniridia (743.45)
essential iris atrophy (364.51)
365.43	Glaucoma associated with other anterior segment anomalies
Code first associated disorder, as:
microcornea (743.41)
365.44	Glaucoma associated with systemic syndromes
Code first associated disease, as:
neurofibromatosis (237.7)
Sturge-Weber (-Dimitri) syndrome (759.6)
365.5	Glaucoma associated with disorders of the lens
365.51	Phacolytic glaucoma
Use additional code for associated hypermature cataract (366.18)
365.52	Pseudoexfoliation glaucoma
Use additional code for associated pseudoexfoliation of capsule (366.11)
365.59	Glaucoma associated with other lens disorders
Use additional code for associated disorder, as:
dislocation of lens (379.33-379.34)
spherophakia (743.36)
365.6	Glaucoma associated with other ocular disorders
365.60	Glaucoma associated with unspecified ocular disorder
365.61	Glaucoma associated with pupillary block
Use additional code for associated disorder, as:
seclusion of pupil [iris bomb�] (364.74)
365.62	Glaucoma associated with ocular inflammations
Use additional code for associated disorder, as:
glaucomatocyclitic crises (364.22)
iridocyclitis (364.0-364.3)
365.63	Glaucoma associated with vascular disorders
Use additional code for associated disorder, as:
central retinal vein occlusion (362.35)
hyphema (364.41)
365.64	Glaucoma associated with tumors or cysts
Use additional code for associated disorder, as:
benign neoplasm (224.0-224.9)
epithelial down-growth (364.61)
malignant neoplasm (190.0-190.9)
365.65	Glaucoma associated with ocular trauma
Use additional code for associated condition, as:
contusion of globe (921.3)
recession of chamber angle (364.77)
365.8	Other specified forms of glaucoma
365.81	Hypersecretion glaucoma
365.82	Glaucoma with increased episcleral venous pressure
365.83	Aqueous misdirection
Malignant glaucoma
365.89	Other specified glaucoma
365.9	Unspecified glaucoma
366	Cataract
Excludes:	congenital cataract (743.30-743.34)
366.0	Infantile, juvenile, and presenile cataract
366.00	Nonsenile cataract, unspecified
366.01	Anterior subcapsular polar cataract
366.02	Posterior subcapsular polar cataract
366.03	Cortical, lamellar, or zonular cataract
366.04	Nuclear cataract
366.09	Other and combined forms of nonsenile cataract
366.1	Senile cataract
366.10	Senile cataract, unspecified
366.11	Pseudoexfoliation of lens capsule
366.12	Incipient cataract
Cataract:
coronary
immature NOS
punctate
Water clefts
366.13	Anterior subcapsular polar senile cataract
366.14	Posterior subcapsular polar senile cataract
366.15	Cortical senile cataract
366.16	Nuclear sclerosis
Cataracta brunescens
Nuclear cataract
366.17	Total or mature cataract
366.18	Hypermature cataract
Morgagni cataract
366.19	Other and combined forms of senile cataract
366.2	Traumatic cataract
366.20	Traumatic cataract, unspecified
366.21	Localized traumatic opacities
Vossius' ring
366.22	Total traumatic cataract
366.23	Partially resolved traumatic cataract
366.3	Cataract secondary to ocular disorders
366.30	Cataracta complicata, unspecified
366.31	Glaucomatous flecks (subcapsular)
Code first underlying glaucoma (365.0-365.9)
366.32	Cataract in inflammatory disorders
Code first underlying condition, as:
chronic choroiditis (363.0-363.2)
366.33	Cataract with neovascularization
Code first underlying condition, as:
chronic iridocyclitis (364.10)
366.34	Cataract in degenerative disorders
Sunflower cataract
Code first underlying condition, as:
chalcosis (360.24)
degenerative myopia (360.21)
pigmentary retinal dystrophy (362.74)
366.4	Cataract associated with other disorders
366.41	Diabetic cataract
Code first diabetes (250.5)
366.42	Tetanic cataract
Code first underlying disease as:
calcinosis (275.40)
hypoparathyroidism (252.1)
366.43	Myotonic cataract
Code first underlying disorder (359.21-359.29)
366.44	Cataract associated with other syndromes
Code first underlying condition, as:
craniofacial dysostosis (756.0)
galactosemia (271.1)
366.45	Toxic cataract
Drug-induced cataract
Use additional E to identify drug or other toxic substance
366.46	Cataract associated with radiation and other physical influences
Use additional E to identify cause
366.5	After-cataract
366.50	After-cataract, unspecified
Secondary cataract NOS
366.51	Soemmering's ring
366.52	Other after-cataract, not obscuring vision
366.53	After-cataract, obscuring vision
366.8	Other cataract
Calcification of lens
366.9	Unspecified cataract
367	Disorders of refraction and accommodation
367.0	Hypermetropia
Far-sightedness
Hyperopia
367.1	Myopia
Near-sightedness
367.2	Astigmatism
367.20	Astigmatism, unspecified
367.21	Regular astigmatism
367.22	Irregular astigmatism
367.3	Anisometropia and aniseikonia
367.31	Anisometropia
367.32	Aniseikonia
367.4	Presbyopia
367.5	Disorders of accommodation
367.51	Paresis of accommodation
Cycloplegia
367.52	Total or complete internal ophthalmoplegia
367.53	Spasm of accommodation
367.8	Other disorders of refraction and accommodation
367.81	Transient refractive change
367.89	Other
Drug-induced disorders of refraction and accommodation
Toxic disorders of refraction and accommodation
367.9	Unspecified disorder of refraction and accommodation
368	Visual disturbances
Excludes:	electrophysiological disturbances (794.11-794.14)
368.0	Amblyopia ex anopsia
368.00	Amblyopia, unspecified
368.01	Strabismic amblyopia
Suppression amblyopia
368.02	Deprivation amblyopia
368.03	Refractive amblyopia
368.1	Subjective visual disturbances
368.10	Subjective visual disturbance, unspecified
368.11	Sudden visual loss
368.12	Transient visual loss
Concentric fading
Scintillating scotoma
368.13	Visual discomfort
Asthenopia
Eye strain
Photophobia
368.14	Visual distortions of shape and size
Macropsia
Metamorphopsia
Micropsia
368.15	Other visual distortions and entoptic phenomena
Photopsia
Refractive:
diplopia
polyopia
Visual halos
368.16	Psychophysical visual disturbances
Visual:
agnosia
disorientation syndrome
hallucinations
368.2	Diplopia
Double vision
368.3	Other disorders of binocular vision
368.30	Binocular vision disorder, unspecified
368.31	Suppression of binocular vision
368.32	Simultaneous visual perception without fusion
368.33	Fusion with defective stereopsis
368.34	Abnormal retinal correspondence
368.4	Visual field defects
368.40	Visual field defect, unspecified
368.41	Scotoma involving central area
Scotoma:
central
centrocecal
paracentral
368.42	Scotoma of blind spot area
Enlarged:
angioscotoma
blind spot
Paracecal scotoma
368.43	Sector or arcuate defects
Scotoma:
arcuate
Bjerrum
Seidel
368.44	Other localized visual field defect
Scotoma:
NOS
ring
Visual field defect:
nasal step
peripheral
368.45	Generalized contraction or constriction
368.46	Homonymous bilateral field defects
Hemianopsia (altitudinal) (homonymous)
Quadrant anopia
368.47	Heteronymous bilateral field defects
Hemianopsia:
binasal
bitemporal
368.5	Color vision deficiencies
Color blindness
368.51	Protan defect
Protanomaly
Protanopia
368.52	Deutan defect
Deuteranomaly
Deuteranopia
368.53	Tritan defect
Tritanomaly
Tritanopia
368.54	Achromatopsia
Monochromatism (cone) (rod)
368.55	Acquired color vision deficiencies
368.59	Other color vision deficiencies
368.6	Night blindness
368.60	Night blindness, unspecified
368.61	Congenital night blindness
Hereditary night blindness
Oguchi's disease
368.62	Acquired night blindness
Excludes:	that due to vitamin A deficiency (264.5)
368.63	Abnormal dark adaptation curve
Abnormal threshold of cones or rods
Delayed adaptation of cones or rods
368.69	Other night blindness
368.8	Other specified visual disturbances
Blurred vision NOS
368.9	Unspecified visual disturbance
369	Blindness and low vision
Excludes:	correctable impaired vision due to refractive errors (367.0-367.9)
Note:	Visual impairment refers to a functional limitation of the eye (e.g., limited visual
 acuity or visual field). It should be distinguished from visual disability, indicating a
 limitation of the abilities of the individual (e.g., limited reading skills, vocational
 skills), and from visual handicap, indicating a limitation of personal and socioeconomic
 independence (e.g., limited mobility, limited employability).
The levels of impairment defined in the table after 369.9 are based on the recommendations
 of the WHO Study Group on Prevention of Blindness (Geneva, November 6-10, 1972; WHO
 Technical Report Series 518), and of the International Council of Ophthalmology (1976).
Note that definitions of blindness vary in different settings.
For international reporting, WHO defines blindness as profound impairment. This definition
 can be applied to blindness of one eye (369.1, 369.6) and to blindness of the individual
 (369.0).
For determination of benefits in the U.S.A., the definition of legal blindness as severe
 impairment is often used.  This definition applies to blindness of the individual only.
369.0	Profound impairment, both eyes
369.00	Impairment level not further specified
Blindness:
NOS according to WHO definition
both eyes
369.01	Better eye:  total impairment; lesser eye:  total impairment
369.02	Better eye:  near-total impairment; lesser eye:  not further specified
369.03	Better eye:  near-total impairment; lesser eye:  total impairment
369.04	Better eye:  near-total impairment; lesser eye:  near-total impairment
369.05	Better eye:  profound impairment; lesser eye:  not further specified
369.06	Better eye:  profound impairment; lesser eye:  total impairment
369.07	Better eye:  profound impairment; lesser eye:  near-total impairment
369.08	Better eye:  profound impairment; lesser eye:  profound impairment
369.1	Moderate or severe impairment, better eye, profound impairment lesser eye
369.10	Impairment level not further specified
Blindness, one eye, low vision other eye
369.11	Better eye:  severe impairment; lesser eye:  blind, not further specified
369.12	Better eye:  severe impairment; lesser eye:  total impairment
369.13	Better eye:  severe impairment; lesser eye:  near-total impairment
369.14	Better eye:  severe impairment; lesser eye:  profound impairment
369.15	Better eye:  moderate impairment; lesser eye:  blind, not further specified
369.16	Better eye:  moderate impairment; lesser eye:  total impairment
369.17	Better eye:  moderate impairment; lesser eye:  near-total impairment
369.18	Better eye:  moderate impairment; lesser eye:  profound impairment
369.2	Moderate or severe impairment, both eyes
369.20	Impairment level not further specified
Low vision, both eyes NOS
369.21	Better eye:  severe impairment; lesser eye:  not further specified
369.22	Better eye:  severe impairment; lesser eye:  severe impairment
369.23	Better eye:  moderate impairment; lesser eye:  not further specified
369.24	Better eye:  moderate impairment; lesser eye:  severe impairment
369.25	Better eye:  moderate impairment; lesser eye:  moderate impairment
369.3	Unqualified visual loss, both eyes
Excludes:	blindness NOS:
legal [U.S.A. definition] (369.4)
WHO definition (369.00)
369.4	Legal blindness, as defined in U.S.A.
Blindness NOS according to U.S.A. definition
Excludes:	legal blindness with specification of impairment level (369.01-369.08,
 369.11-369.14, 369.21-369.22)
369.6	Profound impairment, one eye
369.60	Impairment level not further specified
Blindness, one eye
369.61	One eye:  total impairment; other eye:  not specified
369.62	One eye:  total impairment; other eye:  near-normal vision
369.63	One eye:  total impairment; other eye:  normal vision
369.64	One eye:  near-total impairment; other eye:  not specified
369.65	One eye:  near-total impairment; other eye:  near-normal vision
369.66	One eye:  near-total impairment; other eye:  normal vision
369.67	One eye:  profound impairment; other eye:  not specified
369.68	One eye:  profound impairment; other eye:  near-normal vision
369.69	One eye:  profound impairment; other eye:  normal vision
369.7	Moderate or severe impairment, one eye
369.70	Impairment level not further specified
Low vision, one eye
369.71	One eye:  severe impairment; other eye:  not specified
369.72	One eye:  severe impairment; other eye:  near-normal vision
369.73	One eye:  severe impairment; other eye:  normal vision
369.74	One eye:  moderate impairment; other eye:  not specified
369.75	One eye:  moderate impairment; other eye:  near-normal vision
369.76	One eye:  moderate impairment; other eye:  normal vision
369.8	Unqualified visual loss, one eye
369.9	Unspecified visual loss
----------------------------------------------------------------------
                   |                                   |  Additional 
Classification     |   LEVELS OF VISUAL IMPAIRMENT     |   descriptors
-------------------------------------------------------|   which may 
        |          | Visual acuity and/or visual field |   be en-
"legal" |  WHO     |  limitation (whichever is worse)  |   countered
--------|----------|-----------------------------------|--------------
        |          |                                   |
        |          |     RANGE OF NORMAL VISION        |
        |          | 20/10  20/13  20/16  20/20  20/25 |
        | (NEAR-)  |  2.0    1.6    1.25   1.0    0.8  |
        | NORMAL   |-----------------------------------|--------------
        | VISION   |                                   |
        |          |     NEAR-NORMAL VISION            |
        |          |        20/30  20/40  20/50  20/60 |
        |          |  0.7    0.6    0.5    0.4    0.3  |
        |----------|-----------------------------------|--------------
        |          |     MODERATE VISUAL IMPAIRMENT    |
        |          | 20/70  20/80  20/100 20/125 20/160| Moderate  
        | LOW      |         0.25   0.20   0.16   0.12 |    low vision
--------| VISION   |-----------------------------------|--------------
        |          |     SEVERE VISUAL IMPAIRMENT      | Severe 
        |          | 20/200 20/250 20/320 20/400       |    low vision, 
        |          |  0.10   0.08   0.06   0.05        | "Legal" 
        |          | Visual field: 20 degrees or less  |    blindness
        |----------|-----------------------------------|--------------
LEGAL   |          |      PROFOUND VISUAL IMPAIRMENT   | Profound 
BLIND-  |          | 20/500 20/630 20/800 20/1000      |    low vision, 
NESS    |          |  0.04   0.03   0.025  0.02        | Moderate 
(U.S.A.)|          |                                   |    blindness
        | BLINDNESS|  Count fingers at: less than 3m   | 
        |          |                        (10 ft)    |
        |          |  Visual field: 10 degrees or less |	
        |          |-----------------------------------|--------------
        |          |    NEAR-TOTAL VISUAL IMPAIRMENT   | Severe 
        |          | Visual acuity: less than 0.02     |    blindness,
        |          |                   (20/1000)       | 
        |          |                                   |
both    |  (WHO)   | Count fingers: 1m (3 ft) or less  | 
eyes    |          | Hand movements: 5m (15 ft) or less| Near-total
        |  one or  | Light projection, light perception|    blindness
        |  both    | Visual field: 5 degrees or less   |
        |  eyes    |-----------------------------------|--------------
        |          |    TOTAL VISUAL IMPAIRMENT        | Total 
        |          | No light perception (NLP)         |    blindness
--------|----------|--------------------------------------------------   
Visual acuity refers to best achievable acuity with correction.

Non-listed Snellen fractions may be classified by converting to the nearest decimal
 equivalent, e.g. 10/200 = 0.05, 6/30 = 0.20.

CF (count fingers) without designation of distance, may be classified to profound impairment.

HM (hand motion) without designation of distance, may be classified to near-total impairment.

Visual field measurements refer to the largest field diameter for a 1/100 white test object.

370	Keratitis
370.0	Corneal ulcer
Excludes:	that due to vitamin A deficiency (264.3)
370.00	Corneal ulcer, unspecified
370.01	Marginal corneal ulcer
370.02	Ring corneal ulcer
370.03	Central corneal ulcer
370.04	Hypopyon ulcer
Serpiginous ulcer
370.05	Mycotic corneal ulcer
370.06	Perforated corneal ulcer
370.07	Mooren's ulcer
370.2	Superficial keratitis without conjunctivitis
Excludes:	dendritic [herpes simplex] keratitis (054.42)
370.20	Superficial keratitis, unspecified
370.21	Punctate keratitis
Thygeson's superficial punctate keratitis
370.22	Macular keratitis
Keratitis:
areolar
nummular
stellate
striate
370.23	Filamentary keratitis
370.24	Photokeratitis
Snow blindness
Welders' keratitis
370.3	Certain types of keratoconjunctivitis
370.31	Phlyctenular keratoconjunctivitis
Phlyctenulosis
Use additional code for any associated tuberculosis (017.3)
370.32	Limbar and corneal involvement in vernal conjunctivitis
Use additional code for vernal conjunctivitis (372.13)
370.33	Keratoconjunctivitis sicca, not specified as Sj�gren's
Excludes:	Sj�gren's syndrome (710.2)
370.34	Exposure keratoconjunctivitis
370.35	Neurotrophic keratoconjunctivitis
370.4	Other and unspecified keratoconjunctivitis
370.40	Keratoconjunctivitis, unspecified
Superficial keratitis with conjunctivitis NOS
370.44	Keratitis or keratoconjunctivitis in exanthema
Code first underlying condition (050.0-052.9)
Excludes:	herpes simplex (054.43)
herpes zoster (053.21)
measles (055.71)
370.49	Other
Excludes:	epidemic keratoconjunctivitis (077.1)
370.5	Interstitial and deep keratitis
370.50	Interstitial keratitis, unspecified
370.52	Diffuse interstitial keratitis
Cogan's syndrome
370.54	Sclerosing keratitis
370.55	Corneal abscess
370.59	Other
Excludes:	disciform herpes simplex keratitis (054.43)
syphilitic keratitis (090.3)
370.6	Corneal neovascularization
370.60	Corneal neovascularization, unspecified
370.61	Localized vascularization of cornea
370.62	Pannus (corneal)
370.63	Deep vascularization of cornea
370.64	Ghost vessels (corneal)
370.8	Other forms of keratitis
370.9	Unspecified keratitis
371	Corneal opacity and other disorders of cornea
371.0	Corneal scars and opacities
Excludes:	that due to vitamin A deficiency (264.6)
371.00	Corneal opacity, unspecified
Corneal scar NOS
371.01	Minor opacity of cornea
Corneal nebula
371.02	Peripheral opacity of cornea
Corneal macula not interfering with central vision
371.03	Central opacity of cornea
Corneal:
leucoma interfering with central vision
macula interfering with central vision
371.04	Adherent leucoma
371.05	Phthisical cornea
Code first underlying tuberculosis (017.3)
371.1	Corneal pigmentations and deposits
371.10	Corneal deposit, unspecified
371.11	Anterior pigmentations
St�hli's lines
371.12	Stromal pigmentations
Hematocornea
371.13	Posterior pigmentations
Krukenberg spindle
371.14	Kayser-Fleischer ring
371.15	Other deposits associated with metabolic disorders
371.16	Argentous deposits
371.2	Corneal edema
371.20	Corneal edema, unspecified
371.21	Idiopathic corneal edema
371.22	Secondary corneal edema
371.23	Bullous keratopathy
371.24	Corneal edema due to wearing of contact lenses
371.3	Changes of corneal membranes
371.30	Corneal membrane change, unspecified
371.31	Folds and rupture of Bowman's membrane
371.32	Folds in Descemet's membrane
371.33	Rupture in Descemet's membrane
371.4	Corneal degenerations
371.40	Corneal degeneration, unspecified
371.41	Senile corneal changes
Arcus senilis
Hassall-Henle bodies
371.42	Recurrent erosion of cornea
Excludes:	Mooren's ulcer (370.07)
371.43	Band-shaped keratopathy
371.44	Other calcerous degenerations of cornea
371.45	Keratomalacia NOS
Excludes:	that due to vitamin A deficiency (264.4)
371.46	Nodular degeneration of cornea
Salzmann's nodular dystrophy
371.48	Peripheral degenerations of cornea
Marginal degeneration of cornea [Terrien's]
371.49	Other
Discrete colliquative keratopathy
371.5	Hereditary corneal dystrophies
371.50	Corneal dystrophy, unspecified
371.51	Juvenile epithelial corneal dystrophy
371.52	Other anterior corneal dystrophies
Corneal dystrophy:
microscopic cystic
ring-like
371.53	Granular corneal dystrophy
371.54	Lattice corneal dystrophy
371.55	Macular corneal dystrophy
371.56	Other stromal corneal dystrophies
Crystalline corneal dystrophy
371.57	Endothelial corneal dystrophy
Combined corneal dystrophy
Cornea guttata
Fuchs' endothelial dystrophy
371.58	Other posterior corneal dystrophies
Polymorphous corneal dystrophy
371.6	Keratoconus
371.60	Keratoconus, unspecified
371.61	Keratoconus, stable condition
371.62	Keratoconus, acute hydrops
371.7	Other corneal deformities
371.70	Corneal deformity, unspecified
371.71	Corneal ectasia
371.72	Descemetocele
371.73	Corneal staphyloma
371.8	Other corneal disorders
371.81	Corneal anesthesia and hypoesthesia
371.82	Corneal disorder due to contact lens
Excludes:	corneal edema due to contact lens (371.24)
371.89	Other
371.9	Unspecified corneal disorder
372	Disorders of conjunctiva
Excludes:	keratoconjunctivitis (370.3-370.4)
372.0	Acute conjunctivitis
372.00	Acute conjunctivitis, unspecified
372.01	Serous conjunctivitis, except viral
Excludes:	viral conjunctivitis NOS (077.9)
372.02	Acute follicular conjunctivitis
Conjunctival folliculosis NOS
Excludes:	conjunctivitis:
adenoviral (acute follicular) (077.3)
epidemic hemorrhagic (077.4)
inclusion (077.0)
Newcastle (077.8)
epidemic keratoconjunctivitis (077.1)
pharyngoconjunctival fever (077.2)
372.03	Other mucopurulent conjunctivitis
Catarrhal conjunctivitis
Excludes:	blennorrhea neonatorum (gonococcal) (098.40)
neonatal conjunctivitis (771.6)
ophthalmia neonatorum NOS (771.6)
372.04	Pseudomembranous conjunctivitis
Membranous conjunctivitis
Excludes:	diphtheritic conjunctivitis (032.81)
372.05	Acute atopic conjunctivitis
372.1	Chronic conjunctivitis
372.10	Chronic conjunctivitis, unspecified
372.11	Simple chronic conjunctivitis
372.12	Chronic follicular conjunctivitis
372.13	Vernal conjunctivitis
372.14	Other chronic allergic conjunctivitis
372.15	Parasitic conjunctivitis
Code first underlying disease as:
filariasis (125.0-125.9)
mucocutaneous leishmaniasis (085.5)
372.2	Blepharoconjunctivitis
372.20	Blepharoconjunctivitis, unspecified
372.21	Angular blepharoconjunctivitis
372.22	Contact blepharoconjunctivitis
372.3	Other and unspecified conjunctivitis
372.30	Conjunctivitis, unspecified
372.31	Rosacea conjunctivitis
Code first underlying rosacea dermatitis (695.3)
372.33	Conjunctivitis in mucocutaneous disease
Code first underlying disease as:
erythema multiforme (695.1)
Reiter's disease (099.3)
Excludes:	ocular pemphigoid (694.61)
372.39	Other
372.4	Pterygium
Excludes:	pseudopterygium (372.52)
372.40	Pterygium, unspecified
372.41	Peripheral pterygium, stationary
372.42	Peripheral pterygium, progressive
372.43	Central pterygium
372.44	Double pterygium
372.45	Recurrent pterygium
372.5	Conjunctival degenerations and deposits
372.50	Conjunctival degeneration, unspecified
372.51	Pinguecula
372.52	Pseudopterygium
372.53	Conjunctival xerosis
Excludes:	conjunctival xerosis due to vitamin A deficiency (264.0, 264.1, 264.7)
372.54	Conjunctival concretions
372.55	Conjunctival pigmentations
Conjunctival argyrosis
372.56	Conjunctival deposits
372.6	Conjunctival scars
372.61	Granuloma of conjunctiva
372.62	Localized adhesions and strands of conjunctiva
372.63	Symblepharon
Extensive adhesions of conjunctiva
372.64	Scarring of conjunctiva
Contraction of eye socket (after enucleation)
372.7	Conjunctival vascular disorders and cysts
372.71	Hyperemia of conjunctiva
372.72	Conjunctival hemorrhage
Hyposphagma
Subconjunctival hemorrhage
372.73	Conjunctival edema
Chemosis of conjunctiva
Subconjunctival edema
372.74	Vascular abnormalities of conjunctiva
Aneurysm(ata) of conjunctiva
372.75	Conjunctival cysts
372.8	Other disorders of conjunctiva
372.81	Conjunctivochalasis
372.89	Other disorders of conjunctiva
372.9	Unspecified disorder of conjunctiva
373	Inflammation of eyelids
373.0	Blepharitis
Excludes:	blepharoconjunctivitis (372.20-372.22)
373.00	Blepharitis, unspecified
373.01	Ulcerative blepharitis
373.02	Squamous blepharitis
373.1	Hordeolum and other deep inflammation of eyelid
373.11	Hordeolum externum
Hordeolum NOS
Stye
373.12	Hordeolum internum
Infection of meibomian gland
373.13	Abscess of eyelid
Furuncle of eyelid
373.2	Chalazion
Meibomian (gland) cyst
Excludes:	infected meibomian gland (373.12)
373.3	Noninfectious dermatoses of eyelid
373.31	Eczematous dermatitis of eyelid
373.32	Contact and allergic dermatitis of eyelid
373.33	Xeroderma of eyelid
373.34	Discoid lupus erythematosus of eyelid
373.4	Infective dermatitis of eyelid of types resulting in deformity
Code first underlying disease, as:
leprosy (030.0-030.9)
lupus vulgaris (tuberculous) (017.0)
yaws (102.0-102.9)
373.5	Other infective dermatitis of eyelid
Code first underlying disease, as:
actinomycosis (039.3)
impetigo (684)
mycotic dermatitis (110.0-111.9)
vaccinia (051.0)
postvaccination (999.0)
Excludes:	herpes:
simplex (054.41)
zoster (053.20)
373.6	Parasitic infestation of eyelid
Code first underlying disease, as:
leishmaniasis (085.0-085.9)
loiasis (125.2)
onchocerciasis (125.3)
pediculosis (132.0)
373.8	Other inflammations of eyelids
373.9	Unspecified inflammation of eyelid
374	Other disorders of eyelids
374.0	Entropion and trichiasis of eyelid
374.00	Entropion, unspecified
374.01	Senile entropion
374.02	Mechanical entropion
374.03	Spastic entropion
374.04	Cicatricial entropion
374.05	Trichiasis without entropion
374.1	Ectropion
374.10	Ectropion, unspecified
374.11	Senile ectropion
374.12	Mechanical ectropion
374.13	Spastic ectropion
374.14	Cicatricial ectropion
374.2	Lagophthalmos
374.20	Lagophthalmos, unspecified
374.21	Paralytic lagophthalmos
374.22	Mechanical lagophthalmos
374.23	Cicatricial lagophthalmos
374.3	Ptosis of eyelid
374.30	Ptosis of eyelid, unspecified
374.31	Paralytic ptosis
374.32	Myogenic ptosis
374.33	Mechanical ptosis
374.34	Blepharochalasis
Pseudoptosis
374.4	Other disorders affecting eyelid function
Excludes:	blepharoclonus (333.81)
blepharospasm (333.81)
facial nerve palsy (351.0)
third nerve palsy or paralysis (378.51-378.52)
tic (psychogenic) (307.20-307.23)
organic (333.3)
374.41	Lid retraction or lag
374.43	Abnormal innervation syndrome
Jaw-blinking
Paradoxical facial movements
374.44	Sensory disorders
374.45	Other sensorimotor disorders
Deficient blink reflex
374.46	Blepharophimosis
Ankyloblepharon
374.5	Degenerative disorders of eyelid and periocular area
374.50	Degenerative disorder of eyelid, unspecified
374.51	Xanthelasma
Xanthoma (planum) (tuberosum) of eyelid
Code first underlying condition (272.0-272.9)
374.52	Hyperpigmentation of eyelid
Chloasma
Dyspigmentation
374.53	Hypopigmentation of eyelid
Vitiligo of eyelid
374.54	Hypertrichosis of eyelid
374.55	Hypotrichosis of eyelid
Madarosis of eyelid
374.56	Other degenerative disorders of skin affecting eyelid
374.8	Other disorders of eyelid
374.81	Hemorrhage of eyelid
Excludes:	black eye (921.0)
374.82	Edema of eyelid
Hyperemia of eyelid
374.83	Elephantiasis of eyelid
374.84	Cysts of eyelids
Sebaceous cyst of eyelid
374.85	Vascular anomalies of eyelid
374.86	Retained foreign body of eyelid
374.87	Dermatochalasis
374.89	Other disorders of eyelid
374.9	Unspecified disorder of eyelid
375	Disorders of lacrimal system
375.0	Dacryoadenitis
375.00	Dacryoadenitis, unspecified
375.01	Acute dacryoadenitis
375.02	Chronic dacryoadenitis
375.03	Chronic enlargement of lacrimal gland
375.1	Other disorders of lacrimal gland
375.11	Dacryops
375.12	Other lacrimal cysts and cystic degeneration
375.13	Primary lacrimal atrophy
375.14	Secondary lacrimal atrophy
375.15	Tear film insufficiency, unspecified
Dry eye syndrome
375.16	Dislocation of lacrimal gland
375.2	Epiphora
375.20	Epiphora, unspecified as to cause
375.21	Epiphora due to excess lacrimation
375.22	Epiphora due to insufficient drainage
375.3	Acute and unspecified inflammation of lacrimal passages
Excludes:	neonatal dacryocystitis (771.6)
375.30	Dacryocystitis, unspecified
375.31	Acute canaliculitis, lacrimal
375.32	Acute dacryocystitis
Acute peridacryocystitis
375.33	Phlegmonous dacryocystitis
375.4	Chronic inflammation of lacrimal passages
375.41	Chronic canaliculitis
375.42	Chronic dacryocystitis
375.43	Lacrimal mucocele
375.5	Stenosis and insufficiency of lacrimal passages
375.51	Eversion of lacrimal punctum
375.52	Stenosis of lacrimal punctum
375.53	Stenosis of lacrimal canaliculi
375.54	Stenosis of lacrimal sac
375.55	Obstruction of nasolacrimal duct, neonatal
Excludes:	congenital anomaly of nasolacrimal duct (743.65)
375.56	Stenosis of nasolacrimal duct, acquired
375.57	Dacryolith
375.6	Other changes of lacrimal passages
375.61	Lacrimal fistula
375.69	Other
375.8	Other disorders of lacrimal system
375.81	Granuloma of lacrimal passages
375.89	Other
375.9	Unspecified disorder of lacrimal system
376	Disorders of the orbit
376.0	Acute inflammation of orbit
376.00	Acute inflammation of orbit, unspecified
376.01	Orbital cellulitis
Abscess of orbit
376.02	Orbital periostitis
376.03	Orbital osteomyelitis
376.04	Tenonitis
376.1	Chronic inflammatory disorders of orbit
376.10	Chronic inflammation of orbit, unspecified
376.11	Orbital granuloma
Pseudotumor (inflammatory) of orbit
376.12	Orbital myositis
376.13	Parasitic infestation of orbit
Code first underlying disease, as:
hydatid infestation of orbit (122.3, 122.6, 122.9)
myiasis of orbit (134.0)
376.2	Endocrine exophthalmos
Code first underlying thyroid disorder (242.0-242.9)
376.21	Thyrotoxic exophthalmos
376.22	Exophthalmic ophthalmoplegia
376.3	Other exophthalmic conditions
376.30	Exophthalmos, unspecified
376.31	Constant exophthalmos
376.32	Orbital hemorrhage
376.33	Orbital edema or congestion
376.34	Intermittent exophthalmos
376.35	Pulsating exophthalmos
376.36	Lateral displacement of globe
376.4	Deformity of orbit
376.40	Deformity of orbit, unspecified
376.41	Hypertelorism of orbit
376.42	Exostosis of orbit
376.43	Local deformities due to bone disease
376.44	Orbital deformities associated with craniofacial deformities
376.45	Atrophy of orbit
376.46	Enlargement of orbit
376.47	Deformity due to trauma or surgery
376.5	Enophthalmos
376.50	Enophthalmos, unspecified as to cause
376.51	Enophthalmos due to atrophy of orbital tissue
376.52	Enophthalmos due to trauma or surgery
376.6	Retained (old) foreign body following penetrating wound of orbit
Retrobulbar foreign body
376.8	Other orbital disorders
376.81	Orbital cysts
Encephalocele of orbit
376.82	Myopathy of extraocular muscles
376.89	Other
376.9	Unspecified disorder of orbit
377	Disorders of optic nerve and visual pathways
377.0	Papilledema
377.00	Papilledema, unspecified
377.01	Papilledema associated with increased intracranial pressure
377.02	Papilledema associated with decreased ocular pressure
377.03	Papilledema associated with retinal disorder
377.04	Foster-Kennedy syndrome
377.1	Optic atrophy
377.10	Optic atrophy, unspecified
377.11	Primary optic atrophy
Excludes:	neurosyphilitic optic atrophy (094.84)
377.12	Postinflammatory optic atrophy
377.13	Optic atrophy associated with retinal dystrophies
377.14	Glaucomatous atrophy [cupping] of optic disc
377.15	Partial optic atrophy
Temporal pallor of optic disc
377.16	Hereditary optic atrophy
Optic atrophy:
dominant hereditary
Leber's
377.2	Other disorders of optic disc
377.21	Drusen of optic disc
377.22	Crater-like holes of optic disc
377.23	Coloboma of optic disc
377.24	Pseudopapilledema
377.3	Optic neuritis
Excludes:	meningococcal optic neuritis (036.81)
377.30	Optic neuritis, unspecified
377.31	Optic papillitis
377.32	Retrobulbar neuritis (acute)
Excludes:	syphilitic retrobulbar neuritis (094.85)
377.33	Nutritional optic neuropathy
377.34	Toxic optic neuropathy
Toxic amblyopia
377.39	Other
Excludes:	ischemic optic neuropathy (377.41)
377.4	Other disorders of optic nerve
377.41	Ischemic optic neuropathy
377.42	Hemorrhage in optic nerve sheaths
377.43	Optic nerve hypoplasia
377.49	Other
Compression of optic nerve
377.5	Disorders of optic chiasm
377.51	Associated with pituitary neoplasms and disorders
377.52	Associated with other neoplasms
377.53	Associated with vascular disorders
377.54	Associated with inflammatory disorders
377.6	Disorders of other visual pathways
377.61	Associated with neoplasms
377.62	Associated with vascular disorders
377.63	Associated with inflammatory disorders
377.7	Disorders of visual cortex
Excludes:	visual:
agnosia (368.16)
hallucinations (368.16)
halos (368.15)
377.71	Associated with neoplasms
377.72	Associated with vascular disorders
377.73	Associated with inflammatory disorders
377.75	Cortical blindness
377.9	Unspecified disorder of optic nerve and visual pathways
378	Strabismus and other disorders of binocular eye movements
Excludes:	nystagmus and other irregular eye movements (379.50-379.59)
378.0	Esotropia
Convergent concomitant strabismus
Excludes:	intermittent esotropia (378.20-378.22)
378.00	Esotropia, unspecified
378.01	Monocular esotropia
378.02	Monocular esotropia with A pattern
378.03	Monocular esotropia with V pattern
378.04	Monocular esotropia with other noncomitancies
Monocular esotropia with X or Y pattern
378.05	Alternating esotropia
378.06	Alternating esotropia with A pattern
378.07	Alternating esotropia with V pattern
378.08	Alternating esotropia with other noncomitancies
Alternating esotropia with X or Y pattern
378.1	Exotropia
Divergent concomitant strabismus
Excludes:	intermittent exotropia (378.20, 378.23-378.24)
378.10	Exotropia, unspecified
378.11	Monocular exotropia
378.12	Monocular exotropia with A pattern
378.13	Monocular exotropia with V pattern
378.14	Monocular exotropia with other noncomitancies
Monocular exotropia with X or Y pattern
378.15	Alternating exotropia
378.16	Alternating exotropia with A pattern
378.17	Alternating exotropia with V pattern
378.18	Alternating exotropia with other noncomitancies
Alternating exotropia with X or Y pattern
378.2	Intermittent heterotropia
Excludes:	vertical heterotropia (intermittent) (378.31)
378.20	Intermittent heterotropia, unspecified
Intermittent:
esotropia NOS
exotropia NOS
378.21	Intermittent esotropia, monocular
378.22	Intermittent esotropia, alternating
378.23	Intermittent exotropia, monocular
378.24	Intermittent exotropia, alternating
378.3	Other and unspecified heterotropia
378.30	Heterotropia, unspecified
378.31	Hypertropia
Vertical heterotropia (constant) (intermittent)
378.32	Hypotropia
378.33	Cyclotropia
378.34	Monofixation syndrome
Microtropia
378.35	Accommodative component in esotropia
378.4	Heterophoria
378.40	Heterophoria, unspecified
378.41	Esophoria
378.42	Exophoria
378.43	Vertical heterophoria
378.44	Cyclophoria
378.45	Alternating hyperphoria
378.5	Paralytic strabismus
378.50	Paralytic strabismus, unspecified
378.51	Third or oculomotor nerve palsy, partial
378.52	Third or oculomotor nerve palsy, total
378.53	Fourth or trochlear nerve palsy
378.54	Sixth or abducens nerve palsy
378.55	External ophthalmoplegia
378.56	Total ophthalmoplegia
378.6	Mechanical strabismus
378.60	Mechanical strabismus, unspecified
378.61	Brown's (tendon) sheath syndrome
378.62	Mechanical strabismus from other musculofascial disorders
378.63	Limited duction associated with other conditions
378.7	Other specified strabismus
378.71	Duane's syndrome
378.72	Progressive external ophthalmoplegia
378.73	Strabismus in other neuromuscular disorders
378.8	Other disorders of binocular eye movements
Excludes:	nystagmus (379.50-379.56)
378.81	Palsy of conjugate gaze
378.82	Spasm of conjugate gaze
378.83	Convergence insufficiency or palsy
378.84	Convergence excess or spasm
378.85	Anomalies of divergence
378.86	Internuclear ophthalmoplegia
378.87	Other dissociated deviation of eye movements
Skew deviation
378.9	Unspecified disorder of eye movements
Ophthalmoplegia NOS
Strabismus NOS
379	Other disorders of eye
379.0	Scleritis and episcleritis
Excludes:	syphilitic episcleritis (095.0)
379.00	Scleritis, unspecified
Episcleritis NOS
379.01	Episcleritis periodica fugax
379.02	Nodular episcleritis
379.03	Anterior scleritis
379.04	Scleromalacia perforans
379.05	Scleritis with corneal involvement
Scleroperikeratitis
379.06	Brawny scleritis
379.07	Posterior scleritis
Sclerotenonitis
379.09	Other
Scleral abscess
379.1	Other disorders of sclera
Excludes:	blue sclera (743.47)
379.11	Scleral ectasia
Scleral staphyloma NOS
379.12	Staphyloma posticum
379.13	Equatorial staphyloma
379.14	Anterior staphyloma, localized
379.15	Ring staphyloma
379.16	Other degenerative disorders of sclera
379.19	Other
379.2	Disorders of vitreous body
379.21	Vitreous degeneration
Vitreous:
cavitation
detachment
liquefaction
379.22	Crystalline deposits in vitreous
Asteroid hyalitis
Synchysis scintillans
379.23	Vitreous hemorrhage
379.24	Other vitreous opacities
Vitreous floaters
379.25	Vitreous membranes and strands
379.26	Vitreous prolapse
379.29	Other disorders of vitreous
Excludes:	vitreous abscess (360.04)
379.3	Aphakia and other disorders of lens
Excludes:	after-cataract (366.50-366.53)
379.31	Aphakia
Excludes:	cataract extraction status (V45.61)
379.32	Subluxation of lens
379.33	Anterior dislocation of lens
379.34	Posterior dislocation of lens
379.39	Other disorders of lens
379.4	Anomalies of pupillary function
379.40	Abnormal pupillary function, unspecified
379.41	Anisocoria
379.42	Miosis (persistent), not due to miotics
379.43	Mydriasis (persistent), not due to mydriatics
379.45	Argyll Robertson pupil, atypical
Argyll Robertson phenomenon or pupil, nonsyphilitic
Excludes:	Argyll Robertson pupil (syphilitic) (094.89)
379.46	Tonic pupillary reaction
Adie's pupil or syndrome
379.49	Other
Hippus
Pupillary paralysis
379.5	Nystagmus and other irregular eye movements
379.50	Nystagmus, unspecified
379.51	Congenital nystagmus
379.52	Latent nystagmus
379.53	Visual deprivation nystagmus
379.54	Nystagmus associated with disorders of the vestibular system
379.55	Dissociated nystagmus
379.56	Other forms of nystagmus
379.57	Deficiencies of saccadic eye movements
Abnormal optokinetic response
379.58	Deficiencies of smooth pursuit movements
379.59	Other irregularities of eye movements
Opsoclonus
379.6	Inflammation (infection) of postprocedural bleb
Postprocedural blebitis
379.60	Inflammation (infection) of postprocedural bleb, unspecified
379.61	Inflammation (infection) of postprocedural bleb, stage 1
379.62	Inflammation (infection) of postprocedural bleb, stage 2
379.63	Inflammation (infection) of postprocedural bleb, stage 3
Bleb associated endophthalmitis
379.8	Other specified disorders of eye and adnexa
379.9	Unspecified disorder of eye and adnexa
379.90	Disorder of eye, unspecified
379.91	Pain in or around eye
379.92	Swelling or mass of eye
379.93	Redness or discharge of eye
379.99	Other ill-defined disorders of eye
Excludes:	blurred vision NOS (368.8)

DISEASES OF THE EAR AND MASTOID PROCESS (380-389)

380	Disorders of external ear
380.0	Perichondritis and chondritis of pinna
Chondritis of auricle
Perichondritis of auricle
380.00	Perichondritis of pinna, unspecified
380.01	Acute perichondritis of pinna
380.02	Chronic perichondritis of pinna
380.03	Chondritis of pinna
380.1	Infective otitis externa
380.10	Infective otitis externa, unspecified
Otitis externa (acute):
NOS
circumscribed
diffuse
hemorrhagica
infective NOS
380.11	Acute infection of pinna
Excludes:	furuncular otitis externa (680.0)
380.12	Acute swimmers' ear
Beach ear
Tank ear
380.13	Other acute infections of external ear
Code first underlying disease, as:
erysipelas (035)
impetigo (684)
seborrheic dermatitis (690.10-690.18)
Excludes:	herpes simplex (054.73)
herpes zoster (053.71)
380.14	Malignant otitis externa
380.15	Chronic mycotic otitis externa
Code first underlying disease, as:
aspergillosis (117.3)
otomycosis NOS (111.9)
Excludes:	candidal otitis externa (112.82)
380.16	Other chronic infective otitis externa
Chronic infective otitis externa NOS
380.2	Other otitis externa
380.21	Cholesteatoma of external ear
Keratosis obturans of external ear (canal)
Excludes:	cholesteatoma NOS (385.30-385.35)
postmastoidectomy (383.32)
380.22	Other acute otitis externa
Acute otitis externa:
actinic
chemical
contact
eczematoid
reactive
380.23	Other chronic otitis externa
Chronic otitis externa NOS
380.3	Noninfectious disorders of pinna
380.30	Disorder of pinna, unspecified
380.31	Hematoma of auricle or pinna
380.32	Acquired deformities of auricle or pinna
Excludes:	cauliflower ear (738.7)
380.39	Other
Excludes:	gouty tophi of ear (274.81)
380.4	Impacted cerumen
Wax in ear
380.5	Acquired stenosis of external ear canal
Collapse of external ear canal
380.50	Acquired stenosis of external ear canal, unspecified as to cause
380.51	Secondary to trauma
380.52	Secondary to surgery
380.53	Secondary to inflammation
380.8	Other disorders of external ear
380.81	Exostosis of external ear canal
380.89	Other
380.9	Unspecified disorder of external ear
381	Nonsuppurative otitis media and Eustachian tube disorders
381.0	Acute nonsuppurative otitis media
Acute tubotympanic catarrh
Otitis media, acute or subacute:
catarrhal
exudative
transudative
with effusion
Excludes:	otitic barotrauma (993.0)
381.00	Acute nonsuppurative otitis media, unspecified
381.01	Acute serous otitis media
Acute or subacute secretory otitis media
381.02	Acute mucoid otitis media
Acute or subacute seromucinous otitis media
Blue drum syndrome
381.03	Acute sanguinous otitis media
381.04	Acute allergic serous otitis media
381.05	Acute allergic mucoid otitis media
381.06	Acute allergic sanguinous otitis media
381.1	Chronic serous otitis media
Chronic tubotympanic catarrh
381.10	Chronic serous otitis media, simple or unspecified
381.19	Other
Serosanguinous chronic otitis media
381.2	Chronic mucoid otitis media
Glue ear
Excludes:	adhesive middle ear disease (385.10-385.19)
381.20	Chronic mucoid otitis media, simple or unspecified
381.29	Other
Mucosanguinous chronic otitis media
381.3	Other and unspecified chronic nonsuppurative otitis media
Otitis media, chronic:
allergic
exudative
secretory
seromucinous
transudative
with effusion
381.4	Nonsuppurative otitis media, not specified as acute or chronic
Otitis media:
allergic
catarrhal
exudative
mucoid
secretory
seromucinous
serous
transudative
with effusion
381.5	Eustachian salpingitis
381.50	Eustachian salpingitis, unspecified
381.51	Acute Eustachian salpingitis
381.52	Chronic Eustachian salpingitis
381.6	Obstruction of Eustachian tube
Stenosis of Eustachian tube
Stricture of Eustachian tube
381.60	Obstruction of Eustachian tube, unspecified
381.61	Osseous obstruction of Eustachian tube
Obstruction of Eustachian tube from cholesteatoma, polyp, or other osseous lesion
381.62	Intrinsic cartilagenous obstruction of Eustachian tube
381.63	Extrinsic cartilagenous obstruction of Eustachian tube
Compression of Eustachian tube
381.7	Patulous Eustachian tube
381.8	Other disorders of Eustachian tube
381.81	Dysfunction of Eustachian tube
381.89	Other
381.9	Unspecified Eustachian tube disorder
382	Suppurative and unspecified otitis media
382.0	Acute suppurative otitis media
Otitis media, acute:
necrotizing NOS
purulent
382.00	Acute suppurative otitis media without spontaneous rupture of ear drum
382.01	Acute suppurative otitis media with spontaneous rupture of ear drum
382.02	Acute suppurative otitis media in diseases classified elsewhere
Code first underlying disease, as:
influenza (487.8)
scarlet fever (034.1)
Excludes:	postmeasles otitis (055.2)
382.1	Chronic tubotympanic suppurative otitis media
Benign chronic suppurative otitis media (with anterior perforation of ear drum)
Chronic tubotympanic disease (with anterior perforation of ear drum)
382.2	Chronic atticoantral suppurative otitis media
Chronic atticoantral disease (with posterior or superior marginal perforation of ear drum)
Persistent mucosal disease (with posterior or superior marginal perforation of ear drum)
382.3	Unspecified chronic suppurative otitis media
Chronic purulent otitis media
Excludes:	tuberculous otitis media (017.4)
382.4	Unspecified suppurative otitis media
Purulent otitis media NOS
382.9	Unspecified otitis media
Otitis media:
NOS
acute NOS
chronic NOS
383	Mastoiditis and related conditions
383.0	Acute mastoiditis
Abscess of mastoid
Empyema of mastoid
383.00	Acute mastoiditis without complications
383.01	Subperiosteal abscess of mastoid
383.02	Acute mastoiditis with other complications
Gradenigo's syndrome
383.1	Chronic mastoiditis
Caries of mastoid
Fistula of mastoid
Excludes:	tuberculous mastoiditis (015.6)
383.2	Petrositis
Coalescing osteitis of petrous bone
Inflammation of petrous bone
Osteomyelitis of petrous bone
383.20	Petrositis, unspecified
383.21	Acute petrositis
383.22	Chronic petrositis
383.3	Complications following mastoidectomy
383.30	Postmastoidectomy complication, unspecified
383.31	Mucosal cyst of postmastoidectomy cavity
383.32	Recurrent cholesteatoma of postmastoidectomy cavity
383.33	Granulations of postmastoidectomy cavity
Chronic inflammation of postmastoidectomy cavity
383.8	Other disorders of mastoid
383.81	Postauricular fistula
383.89	Other
383.9	Unspecified mastoiditis
384	Other disorders of tympanic membrane
384.0	Acute myringitis without mention of otitis media
384.00	Acute myringitis, unspecified
Acute tympanitis NOS
384.01	Bullous myringitis
Myringitis bullosa hemorrhagica
384.09	Other
384.1	Chronic myringitis without mention of otitis media
Chronic tympanitis
384.2	Perforation of tympanic membrane
Perforation of ear drum:
NOS
persistent posttraumatic
postinflammatory
Excludes:	otitis media with perforation of tympanic membrane (382.00-382.9)
traumatic perforation [current injury] (872.61)
384.20	Perforation of tympanic membrane, unspecified
384.21	Central perforation of tympanic membrane
384.22	Attic perforation of tympanic membrane
Pars flaccida
384.23	Other marginal perforation of tympanic membrane
384.24	Multiple perforations of tympanic membrane
384.25	Total perforation of tympanic membrane
384.8	Other specified disorders of tympanic membrane
384.81	Atrophic flaccid tympanic membrane
Healed perforation of ear drum
384.82	Atrophic nonflaccid tympanic membrane
384.9	Unspecified disorder of tympanic membrane
385	Other disorders of middle ear and mastoid
Excludes:	mastoiditis (383.0-383.9)
385.0	Tympanosclerosis
385.00	Tympanosclerosis, unspecified as to involvement
385.01	Tympanosclerosis involving tympanic membrane only
385.02	Tympanosclerosis involving tympanic membrane and ear ossicles
385.03	Tympanosclerosis involving tympanic membrane, ear ossicles, and middle ear
385.09	Tympanosclerosis involving other combination of structures
385.1	Adhesive middle ear disease
Adhesive otitis
Otitis media:
chronic adhesive
fibrotic
Excludes:	glue ear (381.20-381.29)
385.10	Adhesive middle ear disease, unspecified as to involvement
385.11	Adhesions of drum head to incus
385.12	Adhesions of drum head to stapes
385.13	Adhesions of drum head to promontorium
385.19	Other adhesions and combinations
385.2	Other acquired abnormality of ear ossicles
385.21	Impaired mobility of malleus
Ankylosis of malleus
385.22	Impaired mobility of other ear ossicles
Ankylosis of ear ossicles, except malleus
385.23	Discontinuity or dislocation of ear ossicles
385.24	Partial loss or necrosis of ear ossicles
385.3	Cholesteatoma of middle ear and mastoid
Cholesterosis of (middle) ear
Epidermosis of (middle) ear
Keratosis of (middle) ear
Polyp of (middle) ear
Excludes:	cholesteatoma:
external ear canal (380.21)
recurrent of postmastoidectomy cavity (383.32)
385.30	Cholesteatoma, unspecified
385.31	Cholesteatoma of attic
385.32	Cholesteatoma of middle ear
385.33	Cholesteatoma of middle ear and mastoid
385.35	Diffuse cholesteatosis
385.8	Other disorders of middle ear and mastoid
385.82	Cholesterin granuloma
385.83	Retained foreign body of middle ear
385.89	Other
385.9	Unspecified disorder of middle ear and mastoid
386	Vertiginous syndromes and other disorders of vestibular system
Excludes:	vertigo NOS (780.4)
386.0	M�ni�re's disease
Endolymphatic hydrops
Lermoyez's syndrome
M�ni�re's syndrome or vertigo
386.00	M�ni�re's disease, unspecified
M�ni�re's disease (active)
386.01	Active M�ni�re's disease, cochleovestibular
386.02	Active M�ni�re's disease, cochlear
386.03	Active M�ni�re's disease, vestibular
386.04	Inactive M�ni�re's disease
M�ni�re's disease in remission
386.1	Other and unspecified peripheral vertigo
Excludes:	epidemic vertigo (078.81)
386.10	Peripheral vertigo, unspecified
386.11	Benign paroxysmal positional vertigo
Benign paroxysmal positional nystagmus
386.12	Vestibular neuronitis
Acute (and recurrent) peripheral vestibulopathy
386.19	Other
Aural vertigo
Otogenic vertigo
386.2	Vertigo of central origin
Central positional nystagmus
Malignant positional vertigo
386.3	Labyrinthitis
386.30	Labyrinthitis, unspecified
386.31	Serous labyrinthitis
Diffuse labyrinthitis
386.32	Circumscribed labyrinthitis
Focal labyrinthitis
386.33	Suppurative labyrinthitis
Purulent labyrinthitis
386.34	Toxic labyrinthitis
386.35	Viral labyrinthitis
386.4	Labyrinthine fistula
386.40	Labyrinthine fistula, unspecified
386.41	Round window fistula
386.42	Oval window fistula
386.43	Semicircular canal fistula
386.48	Labyrinthine fistula of combined sites
386.5	Labyrinthine dysfunction
386.50	Labyrinthine dysfunction, unspecified
386.51	Hyperactive labyrinth, unilateral
386.52	Hyperactive labyrinth, bilateral
386.53	Hypoactive labyrinth, unilateral
386.54	Hypoactive labyrinth, bilateral
386.55	Loss of labyrinthine reactivity, unilateral
386.56	Loss of labyrinthine reactivity, bilateral
386.58	Other forms and combinations
386.8	Other disorders of labyrinth
386.9	Unspecified vertiginous syndromes and labyrinthine disorders
387	Otosclerosis
Includes:	otospongiosis
387.0	Otosclerosis involving oval window, nonobliterative
387.1	Otosclerosis involving oval window, obliterative
387.2	Cochlear otosclerosis
Otosclerosis involving:
otic capsule
round window
387.8	Other otosclerosis
387.9	Otosclerosis, unspecified
388	Other disorders of ear
388.0	Degenerative and vascular disorders of ear
388.00	Degenerative and vascular disorders, unspecified
388.01	Presbyacusis
388.02	Transient ischemic deafness
388.1	Noise effects on inner ear
388.10	Noise effects on inner ear, unspecified
388.11	Acoustic trauma (explosive) to ear
Otitic blast injury
388.12	Noise-induced hearing loss
388.2	Sudden hearing loss, unspecified
388.3	Tinnitus
388.30	Tinnitus, unspecified
388.31	Subjective tinnitus
388.32	Objective tinnitus
388.4	Other abnormal auditory perception
388.40	Abnormal auditory perception, unspecified
388.41	Diplacusis
388.42	Hyperacusis
388.43	Impairment of auditory discrimination
388.44	Recruitment
388.45	Acquired auditory processing disorder
Auditory processing disorder NOS
Excludes:	central auditory processing disorder (315.32)
388.5	Disorders of acoustic nerve
Acoustic neuritis 
Degeneration of acoustic or eighth nerve
Disorder of acoustic or eighth nerve
Excludes:	acoustic neuroma (225.1)
syphilitic acoustic neuritis (094.86)
388.6	Otorrhea
388.60	Otorrhea, unspecified
Discharging ear NOS
388.61	Cerebrospinal fluid otorrhea
Excludes:	cerebrospinal fluid rhinorrhea (349.81)
388.69	Other
Otorrhagia
388.7	Otalgia
388.70	Otalgia, unspecified
Earache NOS
388.71	Otogenic pain
388.72	Referred pain
388.8	Other disorders of ear
388.9	Unspecified disorder of ear
389	Hearing loss
389.0	Conductive hearing loss
Conductive deafness
Excludes:	mixed conductive and sensorineural hearing loss (389.20-389.22)
389.00	Conductive hearing loss, unspecified
389.01	Conductive hearing loss, external ear
389.02	Conductive hearing loss, tympanic membrane
389.03	Conductive hearing loss, middle ear
389.04	Conductive hearing loss, inner ear
389.05	Conductive hearing loss, unilateral
389.06	Conductive hearing loss, bilateral
389.08	Conductive hearing loss of combined types
389.1	Sensorineural hearing loss
Perceptive hearing loss or deafness
Excludes:	abnormal auditory perception (388.40-388.44)
mixed conductive and sensorineural hearing loss (389.20-389.22)
psychogenic deafness (306.7)
389.10	Sensorineural hearing loss, unspecified
389.11	Sensory hearing loss, bilateral
389.12	Neural hearing loss, bilateral
389.13	Neural hearing loss, unilateral
389.14	Central hearing loss
389.15	Sensorineural hearing loss, unilateral
389.16	Sensorineural hearing loss, asymmetrical
389.17	Sensory hearing loss, unilateral
389.18	Sensorineural hearing loss, bilateral
389.2	Mixed conductive and sensorineural hearing loss
Deafness or hearing loss of type classifiable to 389.00-389.08 with type classifiable
 to 389.10-389.18
389.20	Mixed hearing loss, unspecified
389.21	Mixed hearing loss, unilateral
389.22	Mixed hearing loss, bilateral
389.7	Deaf nonspeaking, not elsewhere classifiable
389.8	Other specified forms of hearing loss
389.9	Unspecified hearing loss
Deafness NOS









TABLE OF CONTENTS

Preface

Acknowledgments

Introduction

The ICD-9-CM Coordination and Maintenance Committee

Characteristics of the ICD-9-CM

The Disease Classification

Alphabetical Index of Diseases

Table of Drugs and Chemicals

Index To External Causes of Injury (E Code)

Classification of Procedures

Index to Procedures

Appendix A:
Morphology of Neoplasms


Appendix C:
Classification of Drugs by American Hospital Formulary Services List Number and their ICD-9-CM Equivalents


Appendix D:
Classification of Industrial Accidents According to Agency


Appendix E:
List of Three-Digit Categories






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